Mucopolysaccharides

Mucopolysaccharides dogayen sarƙoƙi ne na ƙwayoyin sukari waɗanda ake samu a cikin jiki duka, galibi a cikin ƙashi da ruwa a kewayen gidajen. An fi kiran su glycosaminoglycans.

Lokacin da jiki ba zai iya rushe mucopolysaccharides ba, yanayin da ake kira mucopolysaccharidoses (MPS) yana faruwa. MPS tana nufin rukuni na cututtukan gado na metabolism. Mutanen da ke da MPS ba su da ko ɗaya, ko isa, na wani abu (enzyme) da ake buƙata don lalata sarƙoƙin kwayar sukari.

Siffofin MPS sun haɗa da:

• MPS I (Ciwon Hurler; Ciwon Hurler-Scheie; Ciwon Scheie)
• MPS II (Hunter ciwo)
• MPS III (Sanfilippo ciwo)
• MPS IV (Morquio ciwo)

Glycosaminoglycans; GAG

Kumar V, Abbas AK, Aster JC. Kwayar cuta. A cikin: Kumar V, Abbas AK, Aster JC, eds. Robbins da Cotran Pathologic Tushen Cutar. 9th ed. Philadelphia, PA: Elsevier Saunders; 2015: babi na 5.

Pyeritz RE. Cututtukan gado na kayan haɗi. A cikin: Goldman L, Schafer AI, eds. Magungunan Goldman-Cecil. 26th ed. Philadelphia, PA: Elsevier; 2020: babi na 244.

Spranger JW. Mucopolysaccharidoses. A cikin: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Littafin koyar da ilimin yara. 21st ed. Philadelphia, PA: Elsevier; 2020: babi 107.