Mawallafi: Marcus Baldwin
Ranar Halitta: 21 Yuni 2021
Sabuntawa: 14 Yiwu 2024
Anonim
Rashin kwayar Prothrombin - Magani
Rashin kwayar Prothrombin - Magani

Rashin kwayar cutar kwayar cuta cuta ce da ke faruwa sakamakon rashin sunadarin cikin jini da ake kira prothrombin. Yana haifar da matsaloli game da daskarewar jini (coagulation). Prothrombin kuma ana kiransa da factor II (factor biyu).

Lokacin da kuka zub da jini, jerin maganganu na faruwa a cikin jiki wanda ke taimakawa yaduwar jini. Wannan tsari shi ake kira coagulation cascade. Ya ƙunshi sunadarai na musamman da ake kira coagulation, ko kuma daskarewa, dalilai. Kuna iya samun damar samun yawan zub da jini idan ɗayan ko fiye daga waɗannan abubuwan sun ɓace ko basa aiki kamar yadda ya kamata.

Prothrombin, ko factor II, na ɗaya daga cikin abubuwan da ke haifar da ciwon coagulation. Rashin kwayar Prothrombin yana gudana ne a cikin dangi (wanda aka gada) kuma yana da matukar wuya. Duk iyaye dole ne su sami zuriya don yada cutar ga yaransu. Tarihin dangi game da cutar zubar jini na iya zama haɗarin haɗari.

Hakanan rashi na Prothrombin na iya zama saboda wani yanayi ko amfani da wasu magunguna. Wannan ana kiran sa rashi prothrombin. Zai iya faruwa ta hanyar:

  • Rashin bitamin K (wasu jariran an haife su da rashi bitamin K)
  • Ciwon hanta mai tsanani
  • Amfani da magunguna wadanda suke hana daskarewa (maganin hana yaduwar jini kamar warfarin)

Kwayar cutar na iya haɗawa da ɗayan masu zuwa:


  • Zuban jini mara kyau bayan haihuwa
  • Zuban jinin haila mai yawa
  • Zubar jini bayan tiyata
  • Zubar jini bayan rauni
  • Bruising a sauƙaƙe
  • Hancin Hancin da baya tsayawa cikin sauki
  • Zuban jini bayan haihuwa

Gwajin da za a iya yi sun hada da:

  • Faɗakarwar Factor II
  • Lokaci na thromboplastin
  • Lokacin Prothrombin (PT)
  • Nazarin hadawa (gwaji na musamman na PTT don tabbatar da karancin prothrombin)

Zaa iya sarrafa jini ta hanyar samun infravenous (IV) infusions na plasma ko maida hankali akan abubuwan daskarewa. Idan baku da bitamin K, zaku iya shan wannan bitamin ta baki, ta hanyar allura a ƙarƙashin fata, ko ta jijiya (ta jijiyoyin wuya).

Idan kana da wannan cuta ta zub da jini, tabbatar cewa:

  • Faɗa wa masu kula da lafiyarku kafin ku sami kowane irin tsari, gami da tiyata da aikin haƙori.
  • Faɗa wa danginku saboda suna iya kamuwa da cuta iri ɗaya amma ba su sani ba tukuna.

Waɗannan albarkatun na iya samar da ƙarin bayani game da rashi na Factor VII:


  • Gidauniyar Hemophilia ta Kasa: Sauran ficananan Matsaloli - www.hemophilia.org/Bleeding-Disorders/Types-of-Bleeding-Disorders/Other-Factor-Deficiencies
  • NIH Cibiyar Bayanai na Kwayar Halitta da Rare - rarediseases.info.nih.gov/diseases/2926/prothrombin-deficiency

Sakamakon yana da kyau tare da magani mai kyau.

Rashin gado na prothrombin shine yanayin rayuwa.

Hangen nesa don samun rashi na prothrombin ya dogara da dalilin. Idan cutar hanta ce ta haifar da shi, sakamakon ya dogara da yadda za a iya magance cutar hanta. Shan karin bitamin K zai magance karancin bitamin K.

Zubar da jini mai tsanani a cikin gabobi na iya faruwa.

Samo magani na gaggawa nan da nan idan ka sami zubar jini na ba da dalili ko na dogon lokaci, ko kuma idan ba za ka iya sarrafa zuban jini ba.

Babu wata sananniyar rigakafin rashin rashi na prothrombin. Lokacin da rashin bitamin K ke haifar, amfani da bitamin K na iya taimakawa.

Hypoprothrombinemia; Rashin Factor II; Dysprothrombinemia


  • Tsarin jini
  • Jinin jini

Gailani D, Wheeler AP, Neff AT. Rare coagulation factor ƙarancin. A cikin: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Ka'idoji da Aiki. 7th ed. Philadelphia, PA: Elsevier; 2018: babi na 137.

Zauren JE. Hemostasis da jinin jini. A cikin: Hall JE, ed. Guyton da Hall Littafin Littattafan Jiki. 13th ed. Philadelphia, PA: Elsevier Saunders; 2016: babi na 37.

Ragni MV. Cutar rashin jini: nakasar rashin ciwan coagulation. A cikin: Goldman L, Schafer AI, eds. Magungunan Goldman-Cecil. 25th ed. Philadelphia, PA: Elsevier Saunders; 2016: babi na 174.

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