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Ranar Halitta: 8 Afrilu 2021
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What is Fuchs’ dystrophy? | Ohio State Medical Center
Video: What is Fuchs’ dystrophy? | Ohio State Medical Center

Fuchs (wanda ake kira "fooks") dystrophy cuta ce ta ido wanda ƙwayoyin halitta waɗanda ke layin ciki na farji a hankali fara mutuwa. Cutar ta fi shafar ido biyu.

Fuchs dystrophy za a iya gado, wanda ke nufin ana iya yada shi daga iyaye zuwa yara. Idan kowane daga cikin iyayenku yana da cutar, kuna da damar 50% na haɓaka yanayin.

Koyaya, yanayin na iya faruwa a cikin mutane ba tare da sanannen tarihin dangin cutar ba.

Fuchs dystrophy yafi kowa a cikin mata fiye da na maza. Matsalolin hangen nesa ba sa bayyana kafin shekara 50 a cikin mafi yawan lokuta. Koyaya, mai ba da sabis na kiwon lafiya na iya iya ganin alamun cutar a cikin mutanen da suka kamu da su ta hanyar 30s ko 40s.

Fuchs dystrophy yana shafar siririn ƙwayoyin sel waɗanda ke layin ɓangaren bayan cornea. Waɗannan ƙwayoyin suna taimakawa fitar da ruwa mai yawa daga cikin ƙwarjin. Yayinda yawancin kwayoyin halitta ke rasa, ruwa yana fara hauhawa a cikin kashin jikin mutum, yana haifar da kumburi da kuma gawar girgije.

Da farko, ruwa na iya tashi yayin bacci, lokacin da ido ya rufe. Yayinda cutar ke kara kamari, kananan kumfa zasu iya haifar. Fuskokin suna girma kuma daga ƙarshe zasu iya karyewa. Wannan yana haifar da ciwon ido. Fuchs dystrophy na iya haifar da sifar cornea ya canza, wanda ke haifar da ƙarin matsalolin gani.


Kwayar cutar na iya haɗawa da:

  • Ciwon ido
  • Kulawar ido ga haske da haske
  • Raunuka ko hangen nesa, da farko kawai da safe
  • Ganin launuka masu launi kewaye da fitilu
  • Ganin hangen nesa cikin yini

Mai ba da sabis na iya bincika Fuchs dystrophy yayin gwajin fitilar fitila.

Sauran gwaje-gwajen da za'a iya yi sun haɗa da:

  • Pachymetry - yana auna kaurin cornea
  • Gwajin microscope na kwayar halitta - yana bawa mai ba da damar duba siririn kwayar halitta wacce ke layi a bayan fatar
  • Ganin jarabawar gani

Ana amfani da dusar ido ko man shafawa wanda ke fitar da ruwa daga cikin gyambon ciki don taimakawa bayyanar cututtukan Fuchs dystrophy.

Idan ciwo mai raɗaɗi ya ɓullo a kan jijiyar wuya, ruwan tabarau mai taushi ko tiyata don ƙirƙirar filato a kan raunukan na iya taimakawa rage ciwo.

Iyakar maganin Fuchs dystrophy shine dashen jiki.

Har zuwa kwanan nan, nau'in da aka fi sani da dasawar mutum yana ratsa keratoplasty. A yayin wannan aikin, ana cire karamin yanki na cornea, yana barin buɗewa a gaban ido.Wani ɗan kwalin cornea da ya dace daga mai ba da gudummawar mutum sai a dinka shi a buɗe a gaban idon.


Wata sabuwar dabara da ake kira endothelial keratoplasty (DSEK, DSAEK, ko DMEK) ta zama zaɓi mafi kyau ga mutanen da ke da matsalar Fuchs dystrophy. A cikin wannan aikin, ana maye gurbin yadudduka na ciki na cornea, maimakon duk yadudduka. Wannan yana haifar da saurin dawowa da ƙananan rikice-rikice. Itungiyoyi galibi basa buƙata.

Fuchs dystrophy yana kara lalacewa akan lokaci. Ba tare da dasawa ba, mutumin da ke da tsananin Fuchs dystrophy na iya zama makaho ko kuma jin ciwo mai tsanani da rage gani sosai.

Matsaloli masu sauƙi na Fuchs dystrophy sau da yawa yakan lalace bayan tiyatar cataract. Kwararren likitan ido zai kimanta wannan haɗarin kuma yana iya canza dabara ko lokacin aikin tiyatar idanun.

Kira mai ba ku sabis idan kuna da:

  • Ciwon ido
  • Senswarewar ido ga haske
  • Jin cewa wani abu yana cikin idonka lokacin da babu komai a can
  • Matsalolin hangen nesa kamar hangen nesa ko hangen nesa
  • Ganin hangen nesa

Babu sanannun rigakafin. Guje wa aikin tiyatar ido ko daukar matakan kariya na musamman a yayin aikin tiyatar na iya jinkirta bukatar dashen gawar.


Fuchs ’dystrophy; Fuchs 'endothelial dystrophy; Fuchs 'dystrophy na tsoka

Folberg R. Idon. A cikin: Kumar V, Abbas AK, Aster JC, eds. Robbins & Cotran Pathologic Tushen Cutar. 10 ed. Philadelphia, PA: Elsevier; 2021: babi na 29.

Patel SV Zuwa ga gwajin gwaji a cikin fuchs endothelial corneal dystrophy: rarrabuwa da matakan sakamako - Bowman Club Lecture 2019. BMJ Buɗe Ido. 2019; 4 (1): e000321. PMID: 31414054 pubmed.ncbi.nlm.nih.gov/31414054/.

Rosado-Adames N, Afshari NA. Cututtukan cututtukan cikin gida. A cikin: Yanoff M, Duker JS, eds. Ilimin lafiyar ido. 5th ed. Philadelphia, PA: Elsevier; 2019: babi na 4.21.

Salmon JF. Cornea. A cikin: Salmon JF, ed. Kanski na Clinical Ophthalmology. 9th ed. Philadelphia, PA: Elsevier; 2020: babi na 7.

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