Spherocytosis na gado: haddasawa, cututtuka da magani

Wadatacce

• Abin da ke haifar da spherocytosis
• Babban bayyanar cututtuka
• Yadda ake yin maganin

Spherocytosis na gado wata cuta ce ta kwayar halitta wacce ke nuna canje-canje a cikin membrane ɗin jinin ja, wanda ke son halakarta, sabili da haka ana ɗaukarsa a matsayin mai ƙarancin jini. Canje-canje a cikin membrana na jajayen ƙwayoyin jini yana sanya su karami da rashin ƙarfi kamar yadda aka saba, ana samun saɓo a cikin saifa.

Spherocytosis cuta ce ta gado, wacce ke tare da mutum daga haihuwa, duk da haka, yana iya ci gaba tare da ƙarancin jini na mawuyacin hali. Don haka, a wasu lokuta ba za a sami alamun bayyanar ba kuma a cikin wasu, ana iya tsinkaye, gajiya, jaundice, faɗaɗa ƙwazo da canje-canje na ci gaba, alal misali.

Kodayake babu magani, spherocytosis yana da magani, wanda dole ne likitan jini ya jagoranta, kuma ana iya nuna maye gurbin folic acid kuma, a cikin mawuyacin yanayi, cire saifa, wanda ake kira splenectomy, don sarrafa cutar .

Abin da ke haifar da spherocytosis

Spherocytosis na gado yana faruwa ne ta hanyar canjin kwayar halitta wanda ke haifar da canji a yawan yawa ko ingancin sunadaran da ke samar da membranes na jajayen ƙwayoyin jinin, wanda aka fi sani da jan jini. Canje-canje a cikin waɗannan sunadarai suna haifar da asarar taurin kai da kariya daga membrane ɗin jinin ja, wanda ke sa su kara lalacewa da ƙaramin girma, kodayake abun da ke ciki iri ɗaya ne, samar da ƙananan jajayen ƙwayayen jiki, tare da keɓaɓɓen fasali da kuma karin launi.

Anemia yana tasowa saboda spherocytes, kamar yadda ake kira jajayen kwayoyin da suka canza a spherocytosis, yawanci ana lalata su a cikin maifa, musamman lokacin da canje-canje ke da mahimmanci kuma akwai raunin sassauci da juriya don wucewa ta microcirculation na jini daga wannan kwayar.

Babban bayyanar cututtuka

Spherocytosis za'a iya rarraba shi azaman mai laushi, matsakaici ko mai tsanani. Sabili da haka, mutanen da ke da ƙananan spherocytosis na iya ba su da wata alama, yayin da waɗanda ke da matsakaiciyar cuta zuwa matsakaiciyar spherocytosis na iya samun nau'o'in alamomi da alamomi daban-daban kamar:

• Anemia mai ɗorewa;
• Gwanin;
• Gajiya da rashin haƙuri ga motsa jiki;
• Bilara yawan bilirubin a cikin jini da jaundice, wanda shine launin rawaya na fata da ƙwayoyin mucous;
• Samuwar duwatsu bilirubin a cikin gallbladder;
• Sizeara girman saifa.

Don bincika spherocytosis na gado, ban da kimantawa na asibiti, masanin jijiyoyin na iya yin odar gwajin jini kamar ƙidayar jini, ƙididdigar reticulocyte, auna bilirubin da shafa jini na gefe wanda ke nuna canje-canje da ke nuni da irin wannan ƙarancin cutar.Hakanan an nuna jarrabawa don raunin osmotic, wanda ke auna juriya na membrane ɗin jinin ja.

Yadda ake yin maganin

Spherocytosis na gado ba shi da magani, duk da haka, masanin jijiyoyin na iya ba da shawarar jiyya da za su iya rage munin cutar da alamomin, gwargwadon bukatun mai haƙuri. Game da mutanen da ba sa nuna alamun cutar, babu takamaiman magani da ya wajaba.

Ana bada shawarar maye gurbin folic acid saboda, saboda karyewar kwayoyin jinin ja, wannan abu yafi zama dole don samuwar sabbin kwayoyin halitta a cikin bargo.

Babban hanyar magani ita ce cire saifa ta hanyar tiyata, wanda galibi ana nuna shi ne ga yara sama da shekaru 5 ko 6 da ke fama da cutar ƙarancin jini, kamar waɗanda ke da haemoglobin ƙasa da 8 mg / dl a ƙidayar jini, ko a ƙasa da 10 mg / dl idan akwai mahimman alamu ko rikitarwa kamar duwatsun mafitsara. Hakanan ana iya yin aikin tiyata a kan yara waɗanda ke da jinkirin ci gaba saboda cutar.

Mutanen da ke shan maganin toka sun fi saurin kamuwa da wasu cututtukan ko kuma thromboses, don haka ana bukatar allurai, irin su pneumococcal, baya ga amfani da ASA wajen sarrafa daskarewar jini. Bincika yadda ake yin tiyatar don cire saifa da kuma kulawar da ta dace.