Duk abin da yakamata ku sani Game da Porphyria Cutanea Tarda

Wadatacce

• Kwayar cututtuka
• Hotunan porphyria cutanea tarda
• Dalilin
• Hanyoyin haɗari
• Faruwar lamarin
• Ganewar asali
• Jiyya
• Outlook

Bayani

Porphyria cutanea tarda (PCT) wani nau'in ciwon mara ne ko rashin jini wanda ke shafar fata. PCT shine ɗayan sanannun nau'ikan porphyria. Wani lokaci ana kiransa zuwa colloquially kamar cutar vampire. Wancan ne saboda mutanen da ke da wannan yanayin sau da yawa suna fuskantar bayyanar cututtuka bayan haɗuwa da hasken rana.

Kwayar cututtuka

Mafi yawan alamun cututtukan porphyria cutanea tarda suna bayyana akan fata. Kwayar cutar ta yau da kullun sun haɗa da:

• blisters a kan fata wanda ke fuskantar rana, ciki har da hannaye, fuska, da hannaye
• photoensitivity, wanda ke nufin fatar ku ta damu da rana
• sirara ko taushi fata
• haɓaka haɓakar gashi, yawanci akan fuska
• kwasfa da tabo na fata
• ja, kumburi, ko itching na fata
• raunuka masu tasowa bayan ƙananan raunin da suka yi wa fata
• hyperpigmentation, wanda ke nufin facin fata ya zama mai duhu
• fitsarin da yafi duhu fiye da al'ada ko launin ruwan kasa mai ja
• hanta lalacewa

Bayan kumfa ya bayyana a fatarka, fatar na iya zama bawo. Hakanan abu ne na yau da kullun don bayyana sau ɗaya idan blisters sun warke.

Abubuwan da ke haifar da rikitarwa suna bayyana a fuska, hannaye, da wuya.

Hotunan porphyria cutanea tarda

Dalilin

Porphyria cutanea tarda na iya haifar da abubuwa daban-daban. Yawanci ana rarraba musabbabin ko dai na asali ko samu.

Mafi yawan cututtukan kwayoyin halitta sun hada da:

• tarihin iyali na porphyria cutanea tarda
• rashin gado na enzyme hanta uroporphyrinogen decarboxylase
• tarihin iyali na cutar hanta ko ciwon hanta
• ironarfin hanta fiye da al'ada

Abubuwan da aka samo asali sun hada da:

• shan giya
• amfani da maganin estrogen
• amfani da magungunan hana daukar ciki
• bayyanar da wasu abubuwan muhalli ko sinadarai, kamar su Orange Agent
• shan baƙin ƙarfe da yawa
• shan taba
• samun ciwon hanta C
• samun HIV

A wasu lokuta, ba zai yuwu a tantance dalilin porphyria cutanea tarda ba.

Hanyoyin haɗari

Kuna cikin haɗarin porphyria cutanea tarda mafi girma idan kuna shan sigari ko amfani da giya. Hakanan kuna iya samun wannan yanayin idan kuna da ciwon hanta C ko HIV.

Kasancewa da wasu sinadarai, kamar su Orange Agent, na iya ƙara haɗarin ka. Wataƙila an fallasa ku da wannan sinadarin idan kun kasance tsoffin sojoji waɗanda suka yi aiki a yankin da ke da Wakilin Orange.

Faruwar lamarin

Porphyria cutanea tarda na iya shafar maza da mata. Yawanci yakan bayyana ne bayan shekara 30, don haka ba kasafai ake samun hakan tsakanin yara ko matasa ba.

Porphyria cutanea tarda yana shafar mutane a duniya kuma ba'a iyakance shi ga wani yanki ko ƙasa ba. An kiyasta cewa mutum 1 daga 10,000 zuwa 25,000 na da wannan yanayin.

Ganewar asali

Likitanka na iya yin gwajin jiki, bincika alamomin, da rikodin tarihin lafiyar ka. Bugu da kari, suna iya amfani da wadannan gwaje-gwajen don bincikar porphyria cutanea tarda:

• gwajin jini
• gwajin fitsari
• gwajin kujeru
• biopsy na fata

Likita zai duba matakan porphyrin da hanta enzymes. Ana iya ba da shawarar gwajin kwayar halitta ga mutanen da ke da tarihin iyali na wannan yanayin.

Jiyya

Maganin porphyria cutanea tarda yana mai da hankali kan sarrafawa da dakatar da alamun. Canjin rayuwa, kamar iyakance shan barasa da shan sigari, na iya taimakawa.

Zaɓuɓɓukan maganin gama gari sun haɗa da:

• phlebotomy, wanda shine cire jini don rage baƙin ƙarfe
• Chloroquine (Aralen)
• hydroxychloroquine (Wuta)
• magungunan ciwo
• masu goge ƙarfe
• magance cututtukan da ke haifar da porphyria cutanea tarda, kamar HCV ko HIV

Phlebotomy yana daya daga cikin magungunan gama gari don porphyria cutanea tarda. Hakanan ana amfani da allunan cutar zazzabin cizon sauro.

Sauye-sauyen salon yau da kullun don magance porphyria cutanea tarda sun hada da:

• guje wa shan giya
• ba shan taba ba
• guje wa hasken rana
• ta amfani da hasken rana
• guje wa rauni ga fata
• ba shan estrogens

Wataƙila dole ne ka sanya abin rufe fuska, dogon hannun riga, da hular hat don kiyaye rana.

Porphyria cutanea tarda na iya kara haɗarin cutar kansar hanta ko kuma cirrhosis, wanda ke lalata hanta. Wannan shine dalilin da ya sa yana da mahimmanci kada ku sha barasa idan kuna da wannan yanayin.

Outlook

Porphyria cutanea tarda yawanci yana shafar manya waɗanda suka girmi shekaru 30. Cutar cuta ce ta jini wacce galibi ke shafar fata. Fatar jikinka na iya zama mai saurin kulawa da rana, saboda haka kana bukatar ka kara yin taka-tsantsan don gujewa rana. Buruji na kowa ne daga wannan yanayin.

Likitanku na iya bayar da shawarar magunguna daban-daban don maganin cututtukan fata. Phlebotomy da allurar rigakafin cutar zazzabin cizon sauro sune mafi yawan hanyoyin zabin magani.

Idan kana neman tallafi, bincika wannan jerin abubuwan da suka fi dacewa game da cututtukan fata na shekara.