Mawallafi: Gregory Harris
Ranar Halitta: 7 Afrilu 2021
Sabuntawa: 19 Agusta 2025
Anonim
Klippel-Trenaunay ciwo - Magani
Klippel-Trenaunay ciwo - Magani

Ciwon Klippel-Trenaunay (KTS) wani yanayi ne wanda ba kasafai ake samun sa ba yayin haihuwa. Ciwon yakan haɗu da tabon ruwan inabi mai tashar jiragen ruwa, yawan ciwan ƙasusuwa da nama mai laushi, da jijiyoyin varicose.

Yawancin lokuta na KTS suna faruwa ba tare da cikakken dalili ba. Koyaya, ana tunanin wasu casesan lokuta ana samun su ta hanyar dangi (wadanda aka gada).

Kwayar cutar KTS sun hada da:

  • Yawancin tabo na ruwan inabi ko wasu matsaloli na jijiyoyin jini, gami da wuraren duhu akan fata
  • Jijiyoyin jijiyoyi (ana iya ganinsu tun suna yara, amma ana iya ganin su daga baya a yarinta ko samartaka)
  • Tafiya mara ƙarfi saboda bambancin tsayi da ƙafa (ɓangaren hannu ya fi tsayi)
  • Kashi, jijiya, ko ciwon jijiya

Sauran alamun bayyanar:

  • Zuban jini daga dubura
  • Jini a cikin fitsari

Mutanen da ke cikin wannan yanayin na iya samun ci gaba da yawa na ƙasusuwa da nama mai laushi. Wannan yana faruwa galibi a ƙafafu, amma kuma yana iya shafar hannaye, fuska, kai, ko gabobin ciki.

Za a iya amfani da dabaru daban-daban na daukar hoto don gano wani canji a tsarin jiki saboda wannan yanayin. Wadannan kuma suna taimakawa wajen yanke shawarar shirin magani. Waɗannan na iya haɗawa da:


  • MRA
  • Endoscopic maganin cirewar thermal
  • X-haskoki
  • CT scans ko CT zane-zane
  • MRI
  • Launi duplex ultrasonography

Duban dan tayi yayin daukar ciki na iya taimakawa wajen gano yanayin.

Organizationsungiyoyi masu zuwa suna ba da ƙarin bayani kan KTS:

  • Supportungiyar Tallafi na Ciwon Cutar Klippel-Trenaunay - k-t.org
  • Gidauniyar Haihuwar asasa - www.birthmark.org

Yawancin mutane da KTS suna da kyau, kodayake yanayin na iya shafar bayyanar su. Wasu mutane suna da matsalolin ƙwaƙwalwa daga yanayin.

Wani lokaci ana iya samun jijiyoyin jini mara kyau a cikin ciki, wanda ƙila za a buƙaci a kimanta shi.

Klippel-Trenaunay-Weber ciwo; KTS; Angio-osteohypertrophy; Hemangiectasia masu cutar hawan jini; Nevus verucosus hypertrophicans; Capillary-lymphatico-venous malformation (CLVM)

Greene AK, Mulliken JB. Rashin lafiyar jijiyoyin jini. A cikin: Rodriguez ED, Losee JE, Neligan PC, eds. Tiyatar Filastik: Volume 3: Craniofacial, Head da Neck Surgery da Pediatric Plastic Surgery. 4th ed. Philadelphia, PA: Elsevier; 2018: babi na 39.


Yanar gizo K-T Support Group. Ka'idodin aikin asibiti na Klippel-Trenaunaysyndrome (KTS). k-t.org/assets/images/content/BCH-Klippel-Trenaunay-Syndrome-Management-Guidelines-1-6-2016.pdf. An sabunta Janairu 6, 2016. An shiga Nuwamba 5, 2019.

Longman RE. Klippel-Trenaunay-Weber ciwo. A cikin: Copel JA, D'Alton ME, Feltovich H, et al, eds. Hoton haihuwa. 2nd ed. Philadelphia, PA: Elsevier; 2018: babi na 131.

McCormick AA, Grundwaldt LJ. Rashin lafiyar jijiyoyin jini. A cikin: Zitelli BJ, McIntire SC, Nowalk AJ, eds. Zitelli da Davis 'Atlas na Ciwon Lafiyar Jiki na Yara. 7th ed. Philadelphia, PA: Elsevier; 2018: babi na 10.

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