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Ranar Halitta: 17 Satumba 2021
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Cardiac Amyloidosis: Brave New World! (Martha Grogan, MD) May 23, 2019
Video: Cardiac Amyloidosis: Brave New World! (Martha Grogan, MD) May 23, 2019

Amyloidosis na Cardiac cuta ce ta lalacewa ta hanyar ajiyar furotin mara kyau (amyloid) a cikin ƙwayar zuciya. Waɗannan kuɗaɗen suna sanya wuya ga zuciya yin aiki daidai.

Amyloidosis wani rukuni ne na cututtuka wanda curin sunadaran da ake kira amyloids ke tashi a jikin jikin mutum. Bayan lokaci, waɗannan sunadarai sun maye gurbin nama na yau da kullun, wanda ke haifar da gazawar gabobin da ke ciki. Akwai siffofin amyloidosis da yawa.

Amyloidosis na Cardiac ("cututtukan zuciya mai wuya") yana faruwa lokacin da amyloid ya ajiye matsayin tsokar zuciya ta al'ada. Wannan shine mafi yawan nau'ikan cututtukan zuciya. Amyloidosis na Cardiac na iya shafar yadda siginonin lantarki ke motsawa cikin zuciya (tsarin tafiyarwa). Wannan na iya haifar da bugun zuciya mara kyau (arrhythmias) da siginar zuciya mara kyau (bugun zuciya).

Ana iya gadon yanayin. Ana kiran wannan amyloidosis na zuciya. Hakanan yana iya haɓaka sakamakon wata cuta kamar nau'in ƙashi da ƙwanƙwasa jini, ko kuma sakamakon wata matsalar likita da ke haifar da kumburi. Amyloidosis na Cardiac ya fi dacewa ga maza fiye da mata. Cutar ba safai ake samu ba a cikin mutane ƙasa da shekara 40.


Wasu mutane na iya samun alamun bayyanar. Lokacin yanzu, alamun cututtuka na iya haɗawa da:

  • Yawan fitsari da daddare
  • Gajiya, rage karfin motsa jiki
  • Palpitations (ji na jin bugun zuciya)
  • Breatharancin numfashi tare da aiki
  • Kumburin ciki, kafafu, idon sawu, ko wani sashi na jiki
  • Matsalar numfashi yayin kwanciya

Alamomin amyloidosis na zuciya suna iya kasancewa da alaƙa da wasu yanayi daban-daban. Wannan na iya sa matsalar ta yi wuyar ganowa.

Alamomin na iya haɗawa da:

  • Sautunan da ba na al'ada ba a cikin huhu (huhun huhu) ko gunaguni na zuciya
  • Ruwan jini wanda yake ƙasa ko sauka idan ka tashi
  • Kara girman jijiyoyin wuya
  • Hanta kumbura

Za a iya yin gwaje-gwaje masu zuwa:

  • Kirji ko hoton CT na ciki (wanda aka yi la'akari da "ma'aunin zinare" don taimakawa gano asali wannan yanayin)
  • Magungunan jijiyoyin zuciya
  • Lantarki (ECG)
  • Echocardiogram
  • Hanyoyin fuska ta maganadisu (MRI)
  • Sanarwar zuciya ta nukiliya (MUGA, RNV)
  • Positron watsi tomography (PET)

ECG na iya nuna matsaloli tare da bugun zuciya ko sigina na zuciya. Hakanan yana iya nuna sigina mara ƙarfi (wanda ake kira "low voltage").


Ana amfani da biopsy na zuciya don tabbatar da ganewar asali. Kwayar halittar wani yanki, kamar ciki, koda, ko kashin baya, galibi ana yin sa kuma.

Mai ba ku kiwon lafiya na iya gaya muku ku yi canje-canje ga abincinku, gami da iyakance gishiri da ruwa.

Kuna iya buƙatar shan kwayoyi na ruwa (diuretics) don taimakawa jikin ku kawar da yawan ruwa. Mai ba da sabis na iya gaya maka ka auna kanka kowace rana. Riba mai nauyin fam 3 ko fiye (kilogram 1 ko fiye) sama da kwana 1 zuwa 2 na iya nufin akwai ruwa mai yawa a jiki.

Ana iya amfani da magunguna da suka haɗa da digoxin, masu toshe tashar calcium, da beta-blockers a cikin mutanen da ke fama da cutar atrial fibrillation. Koyaya, dole ne ayi amfani da magungunan tare da taka tsantsan, kuma dole ne a sa ido kan sashi a hankali. Mutanen da ke da amyloidosis na zuciya na iya zama masu saurin kula da tasirin waɗannan kwayoyi.

Sauran jiyya na iya haɗawa da:


  • Chemotherapy
  • Gyarawa mai juyawa-defibrillator (AICD)
  • Mai ɗaukar hoto, idan akwai matsaloli tare da sigina na zuciya
  • Prednisone, maganin rigakafin kumburi

Ana iya yin tunanin dashen zuciya ga mutanen da ke da wasu nau'o'in amyloidosis waɗanda ke da aikin zuciya mara kyau. Mutanen da ke tare da amyloidosis suna iya buƙatar dashen hanta.

A da, ana zaton amyloidosis na zuciya ba zai iya warkewa kuma yana saurin mutuwa. Koyaya, filin yana canzawa cikin sauri. Amyloidosis daban-daban na iya shafar zuciya ta hanyoyi daban-daban. Wasu nau'ikan sun fi tsanani fiye da wasu. Mutane da yawa yanzu zasu iya tsammanin tsira da ƙwarewar rayuwa mai kyau har tsawon shekaru bayan ganewar asali.

Matsaloli na iya haɗawa da:

  • Fibilillation na atrial ko ƙwaƙwalwar ajiyar zuciya
  • Ciwon zuciya mai narkewa
  • Girman ruwa a cikin ciki (ascites)
  • Sensara hankali ga digoxin
  • Pressureananan hawan jini da jiri daga yawan fitsari (saboda magani)
  • Ciwon sinus na rashin lafiya
  • Kwayar cututtukan cututtukan cututtukan cututtukan zuciya (arrhythmias da ke da alaƙa da lahani mara kyau na motsawa ta cikin ƙwayar tsoka)

Kira mai ba ku sabis idan kuna da wannan matsalar kuma ku ci gaba da sababbin alamun bayyanar kamar:

  • Dizziness lokacin da kuka canza wuri
  • Wuce kima (ruwa)
  • Rage nauyi mai nauyi
  • Sifofin suma
  • Matsaloli masu tsananin numfashi

Amyloidosis - zuciya; Amyloidosis na zuciya ta farko - nau'in AL; Amyloidosis na zuciya ta biyu - nau'in AA; Ciwon zuciya mai wuya; Amyloidosis mai lalata

  • Zuciya - sashi ta tsakiya
  • Tsarin jini
  • Biopsy catheter

Falk RH, Hershberger RE. Latedarfafawa, ƙuntatawa, da infiltrative cardiomyopathies. A cikin: Zipes DP, Libby P, Bonow RO, Mann DL, Tomaselli GF, Braunwald E, eds. Braunwald na Ciwon Zuciya: Littafin rubutu na Magungunan zuciya da jijiyoyin jini. 11th ed. Philadelphia, PA: Elsevier; 2019: babi na 77.

McKenna WJ, Elliott PM. Cututtuka na myocardium da endocardium. A cikin: Goldman L, Schafer AI, eds. Magungunan Goldman-Cecil. 26th ed. Philadelphia, PA: Elsevier; 2020: babi na 54.

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