Mawallafi: William Ramirez
Ranar Halitta: 24 Satumba 2021
Sabuntawa: 1 Yuli 2024
Anonim
What is Eosinophilic Fasciitis?
Video: What is Eosinophilic Fasciitis?

Eosinophilic fasciitis (EF) ciwo ne wanda nama a ƙarƙashin fata da kan tsoka, wanda ake kira fascia, ya zama kumbura, mai kumburi da kauri. Fatar jikin hannaye, kafafu, wuya, ciki ko ƙafa na iya kumbura da sauri. Yanayin yana da wuya sosai.

EF na iya yin kama da scleroderma, amma ba shi da alaƙa. Ba kamar scleroderma ba, a cikin EF, yatsun ba su da hannu.

Ba a san dalilin EF ba. Ananan lamura sun faru bayan shan abubuwan karin L-tryptophan. A cikin mutanen da ke da wannan yanayin, fararen ƙwayoyin jini, waɗanda ake kira eosinophils, suna haɓaka a cikin tsokoki da kyallen takarda. Eosinophils yana da alaƙa da halayen rashin lafiyan. Ciwon ya fi zama ruwan dare a cikin mutane masu shekaru 30 zuwa 60.

Kwayar cutar na iya haɗawa da:

  • Jin taushi da kumburin fata akan hannaye, ƙafafu, ko wani lokacin haɗuwa (galibi a kowane ɓangaren jiki)
  • Amosanin gabbai
  • Ciwon ramin rami na carpal
  • Ciwon tsoka
  • Fata mai kauri wanda yayi kama

Gwajin da za a iya yi sun hada da:

  • CBC tare da bambanci
  • Gamma globulins (nau'in furotin ne na tsarin garkuwar jiki)
  • Erythrocyte sedimentation kudi (ESR)
  • MRI
  • Gwajin tsoka
  • Biopsy na fata (biopsy yana buƙatar haɗa da zurfin nama na fascia)

Ana amfani da Corticosteroids da sauran magunguna masu hana rigakafi don taimakawa bayyanar cututtuka. Wadannan magunguna sun fi tasiri idan aka fara su a farkon cutar. Magungunan anti-inflammatory na nonsteroidal (NSAIDs) na iya taimakawa rage alamun.


A mafi yawan lokuta, yanayin yakan tafi tsakanin shekara 1 zuwa 3. Koyaya, bayyanar cututtuka na iya daɗewa ko dawowa.

Arthritis cuta ce mai wahala ta EF. Wasu mutane na iya haifar da mummunar cuta ta jini ko cututtukan da ke da alaƙa da jini, kamar su anemia ko leukemia. Hangen nesa ya fi muni idan cututtukan jini suna faruwa.

Kira mai ba da sabis na kiwon lafiya idan kuna da alamun wannan cuta.

Babu sanannun rigakafin.

Ciwon Shulman

  • Musclesananan tsokoki na baya

Aronson JK. Gwada. A cikin: Aronson JK, ed. Hanyoyin Meyler na Magunguna. 16th ed. Waltham, MA: Elsevier BV ;; 2016: 220-221.

James WD, Elston DM, Kula da JR, Rosenbach MA, Neuhaus IM. Cutar cututtukan nama. A cikin: James WD, Elston DM, Kula da JR, Rosenbach MA, Neuhaus IM, eds. Cututtukan Andrews na Fata: Clinical Dermatology. 13th ed. Philadelphia, PA: Elsevier; 2020: babi na 8.


Lee LA, Werth VP. Fata da cututtukan rheumatic. A cikin: Firestein GS, Budd RC, Gabriel SE, McInnes IB, O'Dell JR, eds. Littafin Kelley da Firestein na Rheumatology. 10 ed. Philadelphia, PA: Elsevier; 2017: babi na 43.

Pinal-Fernandez I, Selva-O 'Callaghan A, Grau JM. Ganewar asali da rarrabuwa na fasciitis eosinophilic. Autoimmun Rev.. 2014; 13 (4-5): 379-382. PMID: 24424187 www.ncbi.nlm.nih.gov/pubmed/24424187.

Nationalungiyar forasa don Rare Rashin Lafiya. Eosinophilic fasciitis. rarediseases.org/rare-diseases/eosinophilic-fasciitis/. An sabunta 2016. An shiga Maris 6, 2017.

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