Rashin factor Factor X

Rashin Factor X (goma) cuta ce ta rashin rashin furotin da ake kira factor X a cikin jini. Yana haifar da matsaloli game da daskarewar jini (coagulation).

Lokacin da kuka zub da jini, jerin maganganu na faruwa a cikin jiki wanda ke taimakawa yaduwar jini. Wannan tsari shi ake kira coagulation cascade. Ya ƙunshi sunadarai na musamman da ake kira coagulation, ko kuma daskarewa, dalilai. Kuna iya samun damar samun yawan zub da jini idan ɗayan ko fiye daga waɗannan abubuwan sun ɓace ko basa aiki kamar yadda ya kamata.

Factor X shine irin wannan nau'in coagulation. Arancin Factor X yawanci ana haifar dashi ne ta hanyar raunin gado a cikin yanayin X gene. Wannan ana kiransa raunin factor X. Zuban jini ya fito ne daga mara nauyi zuwa mai tsanani dangane da yadda karancin yake da tsananin.

Hakanan ƙarancin Factor X na iya zama saboda wani yanayin ko amfani da wasu magunguna. Wannan ana kiran sa raunin factor X. Samun rashi factor X gama gari ne. Zai iya faruwa ta hanyar:

• Rashin bitamin K (wasu jariran an haife su da rashi bitamin K)
• Buildup na sunadarai mara kyau a cikin kyallen takarda da gabobin (amyloidosis)
• Ciwon hanta mai tsanani
• Amfani da magunguna wadanda suke hana daskarewa (maganin hana yaduwar jini kamar warfarin)

Matan da ke da rashi na factor X na farko za a iya bincikar su lokacin da suke jinin al'ada mai nauyi da zub da jini bayan haihuwa. Ana iya fara lura da yanayin ga yara maza da aka haifa idan sun yi jini wanda ya daɗe fiye da yadda aka saba bayan kaciya.

Kwayar cutar na iya haɗawa da ɗayan masu zuwa:

• Zuban jini a cikin gidajen
• Zuban jini a cikin tsokoki
• Bruising a sauƙaƙe
• Zuban jinin haila mai yawa
• Zubar da membrane na jini
• Hancin Hancin da baya tsayawa cikin sauki
• Zuban jini bayan haihuwa

Gwajin da za a iya yi sun hada da:

• Factor X gwaji
• Lokaci na thromboplastin (PTT)
• Lokacin Prothrombin (PT)

Zaa iya sarrafa jini ta hanyar samun infravenous (IV) infusions na plasma ko maida hankali akan abubuwan daskarewa. Idan baku da bitamin K, likitanku zai rubuta muku bitamin K ku sha ta baki, ta hanyar allura a ƙarƙashin fata, ko ta jijiya (ta jijiyoyin wuya).

Idan kana da wannan cuta ta zub da jini, tabbatar cewa:

• Faɗa wa masu kula da lafiyarku kafin ku sami kowane irin tsari, gami da tiyata da aikin haƙori.
• Faɗa wa danginku saboda suna iya kamuwa da cuta iri ɗaya amma ba su sani ba tukuna.

Waɗannan albarkatun na iya samar da ƙarin bayani game da rashi factor X:

• Gidauniyar Hemophilia ta Kasa: Sauran ficananan Matsaloli - www.hemophilia.org/Bleeding-Disorders/Types-of-Bleeding-Disorders/Other-Factor-Deficiencies
• Nationalungiyar forasa don Rare Rashin Lafiya --rarediseases.org/rare-diseases/factor-x-deficiency
• NIH Tsarin Gida na Gida - ghr.nlm.nih.gov/condition/factor-x-deficiency

Sakamakon yana da kyau idan yanayin yayi sauki ko kuma kun sami magani.

Rashin gadon rashi X shine yanayin rayuwa.

Hangen nesa don raunin factor X ya dogara da dalilin. Idan cutar hanta ce ta haifar da shi, sakamakon ya dogara da yadda za a iya magance cutar hanta. Shan karin bitamin K zai magance karancin bitamin K. Idan amyloidosis ne ya haifar da matsalar, akwai zaɓuɓɓukan magani da yawa. Likitanku na iya gaya muku ƙarin bayani.

Zubar jini mai tsanani ko zubar jini ba zato ba tsammani (zubar jini) na iya faruwa. Abubuwan haɗin gwiwa na iya samun nakasa cikin cuta mai tsanani daga yawan zubar jini.

Nemi taimakon gaggawa na gaggawa idan kana da asarar jini na rashin sani ko kuma mai tsanani.

Babu wata sananniyar rigakafi don rashi factor X rashi. Lokacin da rashin bitamin K ke haifar, amfani da bitamin K na iya taimakawa.

Rashin Stuart-Prower

• Tsarin jini
• Jinin jini

Gailani D, Wheeler AP, Neff AT. Rare coagulation factor ƙarancin. A cikin: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Ka'idoji da Aiki. 7th ed. Philadelphia, PA: Elsevier; 2018: babi na 137.

Zauren JE. Hemostasis da jinin jini. A cikin: Hall JE, ed. Guyton da Hall Littafin Littattafan Jiki. 13th ed. Philadelphia, PA: Elsevier; 2016: babi na 37.

Ragni MV. Cutar rashin jini: nakasar rashin ciwan coagulation. A cikin: Goldman L, Schafer AI, eds. Magungunan Goldman-Cecil. 25th ed. Philadelphia, PA: Elsevier Saunders; 2016: babi na 174.