Outofar madaidaiciya madaidaiciya biyu

Outwararren madaidaiciyar madaidaiciyar dama (DORV) cuta ce ta zuciya wanda yake kasancewa tun daga haihuwa (haifuwa). Aorta yana haɗuwa da hagu na dama (RV, ɗakin zuciyar da ke tura jini mai ƙarancin oxygen zuwa huhu), maimakon zuwa hagu na hagu (LV, ɗakin da ke tsinkayar jini mai wadataccen oxygen zuwa jiki).

Dukkanin jijiyoyin huhu (wanda ke daukar jini mara ƙaran oxygen zuwa huhu) da kuma aorta (wanda ke ɗaukar wadataccen jini mai wadataccen oxygen daga zuciya zuwa jiki) sun fito daga ɗakunan yin famfo ɗaya. Babu jijiyoyin da ke haɗe da hagu na hagu (ɗakin da yake tsinkayar jini a jiki).

A cikin tsarin zuciya na yau da kullun, aorta yana haɗuwa da LV. Jijiyar huhu na al'ada tana haɗuwa da RV. A cikin DORV, duka jijiyoyin suna kwarara daga RV. Wannan matsala ce saboda RV yana ɗauke da jini mara kyau na oxygen. Wannan jini ana zagayawa cikin jiki duka.

Wani lahani da ake kira lalatacciyar septal flaft (VSD) koyaushe yana faruwa tare da DORV.

Jini mai wadataccen oxygen daga huhu yana gudana daga gefen hagu na zuciya, ta buɗewar VSD da cikin RV. Wannan yana taimaka wa jariri da DORV ta barin jini mai wadataccen oxygen ya haɗu da jini mara ƙaran oxygen. Ko da wannan cakudawar, jiki bazai sami isashshen oxygen ba. Wannan yana sa zuciya tayi aiki tuƙuru don biyan buƙatun jiki. Akwai nau'ikan DORV da yawa.

Bambanci tsakanin waɗannan nau'ikan shine wurin VSD kamar yadda yake dangane da wurin jijiyar huhu da aorta. Alamomin cutar da tsananin matsalar zasu dogara da nau'in DORV. Kasancewar bugun bawul na huhu kuma yana shafar yanayin.

Mutanen da ke da DORV galibi suna da wasu lahani na zuciya, kamar:

• Launin matashi na endocardial (bangon da ke raba dukkan ɗakuna huɗu na zuciya yana da ƙarancin tsari ko ba ya nan)
• Coarctation na aorta (takaita aorta)
• Matsaloli bawul na mitral
• Pulmonary atresia (bawul na huhu ba ya zama yadda yakamata)
• Ciwon bawul na huhu (taƙaitaccen bawul na huhu)
• Hanyar baka mai dama-dama (baka mai kyau tana kan dama maimakon hagu)
• Sanya manyan jijiyoyi (jijiyoyin jijiyoyin jini da na huhu sun canza)

Alamomin DORV na iya haɗawa da:

• Fadada zuciya
• Zuciyar zuciya
• Saurin numfashi
• Saurin bugun zuciya

Kwayar cutar DORV na iya haɗawa da:

• Rashin ciyarwa daga gajiya cikin sauki
• Bullar launin fata da lebe
• Sanya kumburi (kaurin gadaje na ƙusa) na yatsun kafa da yatsu (alamar ƙarshe)
• Rashin samun nauyi da girma
• Launi mai launi
• Gumi
• Legsafafun kumbura ko ciki
• Matsalar numfashi

Gwaje-gwaje don tantance DORV sun haɗa da:

• Kirjin x-ray
• Duban dan tayi na zuciya (echocardiogram)
• Wuce sirara, sassauƙan bututu zuwa cikin zuciya don auna karfin jini da allurar fenti don hotuna na musamman na zuciya da jijiyoyin jini (catheterization na zuciya)
• Zuciya MRI

Jiyya na buƙatar tiyata don rufe rami a cikin zuciya da kuma kai tsaye jini daga hagu zuwa cikin aorta. Hakanan ana iya buƙatar yin aikin tiyata don matsar da jijiya ko huhu.

Abubuwan da ke tantance nau'in da yawan ayyukan da jaririn ke buƙata sun haɗa da:

• Nau'in DORV
• Tsananin lahani
• Kasancewar sauran matsaloli a cikin zuciya
• Yarinyar gabaɗaya

Ta yaya jariri yayi kyau ya dogara da:

• Girman da wurin VSD
• Girman ɗakunan yin famfo
• Yanayin bugun aorta da jijiyar huhu
• Kasancewar akwai wasu matsaloli (kamar su haɗuwar aorta da matsalolin bawul na mitral)
• Lafiyar jariri gabaɗaya a lokacin da aka gano shi
• Ko lalacewar huhu ta faru ne daga yawan jini da ke kwarara zuwa huhu na dogon lokaci

Matsaloli daga DORV na iya haɗawa da:

• Ajiyar zuciya
• Hawan jini a cikin huhu, wanda ba a magance shi ba na iya haifar da cutar huhu na dindindin
• Mutuwa

Yara da ke da wannan yanayin na zuciya na iya buƙatar shan ƙwayoyin cuta kafin maganin haƙori. Wannan yana hana cututtuka a kusa da zuciya. Hakanan ana iya buƙatar maganin rigakafi bayan tiyata.

Kira wa mai ba da lafiyar ku idan yaro ya gajiya da sauƙi, yana da matsalar numfashi, ko yana da fata mai laushi ko leɓɓa. Hakanan yakamata ku tuntuɓi mai ba ku idan jaririnku ba ya girma ko yana da nauyi.

DORV; Taussig-Bing ba da izini ba; DORV tare da VSD sau biyu; DORV tare da VSD da ba a ba da izini ba; DORV tare da subaortic VSD; Ciwon zuciya na haihuwa - DORV; Ciwon zuciya na Cyanotic - DORV; Lalacewar haihuwa - DORV

• Outofar madaidaiciya madaidaiciya biyu

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