Yadda za a magance phenylketonuria da yadda za a guje wa rikitarwa

Wadatacce

• 1. Maganin abinci mai gina jiki
• Yadda ake bada nono lafiya
• 2. Amfani da kayan abinci masu gina jiki
• Matsaloli da ka iya faruwa na phenylketonuria
• Yadda za a guji

Kulawa da jinyar cutar ta phenylketonuria a cikin jariri ya kamata ya zama jagorar likitan yara, amma babban kulawa shine a guji abinci mai wadataccen sinadarin phenylalanine, waɗanda galibi abinci ne masu ɗauke da sunadarai, kamar nama, kifi, madara, cuku da kwai. Don haka, iyayen jarirai masu cutar phenylketonuria ya kamata su mai da hankali ga abincin ɗansu, a gida da makaranta.

Bugu da kari, shayar da nonon uwa zalla ya kamata kuma ya zama ya dace da likitan yara, tunda madarar nono tana dauke da sinadarin phenylalanine, kodayake ya yi kasa da wanda ake samu a mafi yawan magungunan magani. Yakamata, adadin phenylalanine ga jariri har zuwa watanni 6 ya kamata a kiyaye tsakanin 20 zuwa 70 MG na phenylalanine a kowace kilogiram na nauyin jiki.

Yana da mahimmanci cewa ana bin magani don phenylketonuria bisa ga ka'idojin likitan yara da mai gina jiki don hana rikice-rikice daga tasowa, waɗanda galibi suna da alaƙa da ci gaban tsarin juyayi.

1. Maganin abinci mai gina jiki

Maganin abinci mai gina jiki shine babbar hanyar kaucewa rikitarwa na cutar, tunda ta hanyar abinci ne ake iya sarrafa matakan phenylalanine a cikin jini, don haka guje wa rikitarwa na cutar. Yana da mahimmanci cewa abincin ya kasance mai jagorantar mai gina jiki bisa ga sakamakon gwajin jariri waɗanda dole ne a yi su akai-akai don tantance matakan phenylalanine a cikin jini.

Ana iya samun Phenylalanine a cikin abinci da yawa, na dabba da na kayan lambu. Don haka, don magance cutar da guje wa rikitarwa yana da mahimmanci a guji wasu abinci, kamar:

• Abincin dabbobi: nama, madara da kayan nama, kwai, kifi, abincin teku, da kayan naman alade kamar alade, tsiran alade, naman alade, naman alade.
• Abincin asalin shuka: alkama, waken soya da kayan alatu, kaji, wake, wake, wake, gyada, gyada, gyada, almond, hazelnuts, pistachios, pine nuts;
• Abincin zaki tare da aspartame;
• Samfurori waɗanda ke ƙunshe da abincin da aka hana a matsayin sashikamar su waina, da cookies, da ice cream da kuma waina.

'Ya'yan itace da kayan marmari ana iya cinye su ta hanyar phenylketonurics, da sukari da mai. Haka kuma yana yiwuwa a sami samfuran kasuwa na musamman da yawa waɗanda aka yi don wannan masu sauraro, kamar shinkafa, taliya da faski, kuma akwai girke-girke da yawa waɗanda za a iya amfani da su don samar da abinci mai ƙarancin abu a cikin phenylalanine.

Duba jerin abincin da ke cike da sinadarin phenylalanine.

Yadda ake bada nono lafiya

Kodayake shawarwarin shine ware madara nono daga abincin jariri, ta amfani da madarar kantin magani kawai ba tare da phenylalanine ba, har yanzu yana yiwuwa a shayar da jariri phenylketonuric, amma saboda wannan ya zama dole:

• Yi gwajin jini akan jariri kowane mako don bincika matakan phenylalanine a cikin jini;
• Lissafa yawan nonon da za a baiwa jariri, gwargwadon kimar sinadarin phenylalanine da ke cikin jinin jariri kuma bisa ga jagorancin likitan yara;
• Lissafa yawan madarar kantin magani ba tare da phenylalanine ba, don kammala ciyar da jariri;
• Tare da famfo, cire ainihin adadin ruwan nono wanda uwa zata iya baiwa jariri;
• Yi amfani da kwalba ko maimaita fasaha don ciyar da jariri.

Yana da mahimmanci a cire amino acid phenylalanine daga abinci, don kada jariri ya sami matsala a ci gaban jiki da tunani, kamar raunin hankali. Duba yadda abinci yakamata ya kasance a cikin phenylketonuria.

2. Amfani da kayan abinci masu gina jiki

Kamar yadda abincin mai cutar phenylketonuria yake da takura, zai yuwu bashi da yawan bitamin da kuma ma'adanai da ake buƙata don gudanar da ayyukan kwayar da kyau da kuma ci gaban yaro daidai. Don haka, masanin abinci mai gina jiki na iya ba da shawarar yin amfani da abubuwan kari da na abinci mai gina jiki don tabbatar da haɓakar jariri ta dace da inganta lafiyarta.

Supplementarin da za a yi amfani da shi ya nuna ta ƙwararren mai gina jiki gwargwadon shekaru, nauyin mutum da ƙarfin narkewar jariri, kuma dole ne a kiyaye shi tsawon rayuwa.

Matsaloli da ka iya faruwa na phenylketonuria

Rikitarwa na phenylketonuria na tasowa lokacin da ba'a gano cutar da wuri ba ko lokacin da ba a bin magani bisa ga jagororin likitan yara, tare da tarin phenylalanine a cikin jini, wanda zai iya isa takamaiman yankuna na kwakwalwa kuma ya haifar da ci gaba da canje-canje na dindindin, kamar kamar yadda:

• Jinkiri a ci gaban psychomotor;
• Developmentaramar ƙwaƙwalwar ƙwaƙwalwa;
• Microcephaly;
• Rashin hankali;
• Rashin halayyar ɗabi’a;
• Rage IQ;
• Tsanani na rashin hankali;
• Raɗaɗɗu;
• Girgizar ƙasa.

Bayan lokaci, idan ba a kula da yaron yadda ya kamata ba, za a iya samun matsala wajen zama da tafiya, rikicewar halayyar mutum da jinkirta magana da ci gaban ilimi, ban da baƙin ciki, farfadiya da ataxia, wanda shi ne rashin iko. Na ƙungiyoyin son rai.

Yadda za a guji

Don kaucewa rikitarwa, yana da mahimmanci a gano asalin cutar a kwanakin farko bayan haihuwar yaron ta hanyar gwajin dunduniyar diddige. Idan sakamakon ya zama tabbatacce, yana da mahimmanci a yi magani bisa ga jagorancin likitan yara.

Bugu da ƙari, a cikin waɗannan sharuɗɗan yana da mahimmanci a gudanar da bincike na yau da kullun don bincika lafiyar lafiyar yaron kuma, don haka, don nuna canje-canje a cikin abincin da ake ci da abubuwan abinci.

Yawancin lokuta ana yin gwaje-gwaje na mako-mako har sai jaririn ya cika shekara 1. Yaran da ke tsakanin shekara 2 zuwa 6 suna maimaita jarrabawar kowane kwana 15 kuma, daga shekara 7, ana yin jarabawar sau ɗaya a wata.