Mawallafi: Morris Wright
Ranar Halitta: 1 Afrilu 2021
Sabuntawa: 23 Satumba 2024
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Wadatacce

Hemochromatosis cuta ce wacce a cikin ta akwai ƙarfe mai yawa a jiki, yana taimakawa tarawar wannan ma'adinan a cikin gabobin jiki daban-daban da kuma bayyanar rikitarwa kamar ciwan hanta, ciwon sukari, yin duhun fata, ciwon zuciya, ciwon haɗin gwiwa ko glandon aiki, misali.

Maganin hemochromatosis ana nuna shi ta likitan jini, tare da phlebotomies, wanda ake cire su lokaci-lokaci daga jini don a jujjuya baƙin ƙarfe zuwa sabbin jajayen ƙwayoyin jinin da jiki yake samarwa, kuma a wasu lokuta yin amfani da chelatan daga jiki na iya Hakanan za'a iya nuna ƙarfe, kamar yadda suke taimakawa wajen kawar dashi.

Hemochromatosis bayyanar cututtuka

Alamun Hemochromatosis suna tashi yayin da matakan ƙarfe da ke zagaye a cikin jini suka yi yawa sosai, wanda ke haifar da sanya shi a cikin wasu gabobin kamar hanta, zuciya, ƙoshin ciki, fata, haɗin gwiwa, ƙwaraji, ƙwai, ƙyamar gyada da kuma gland. Don haka, manyan alamu da alamun da zasu iya bayyana sune:


  • Gajiya;
  • Rashin rauni;
  • Cirrhosis na hanta;
  • Ciwon suga;
  • Rashin zuciya da arrhythmias;
  • Hadin gwiwa;
  • Rashin jinin haila.

Bugu da kari, a wasu yanayi, yawan ƙarfe na iya haifar da ƙarancin jima'i, rashin haihuwa da hypothyroidism. San wasu alamun da ke nuna yawan ƙarfe.

Yadda ake ganewar asali

Ganewar cutar ta hemacromatosis ana yin ta ne ta hanyar kimanta alamomi da gwaje-gwajen jini da likitan jini ko babban likita ya nuna don tantance matakan ƙarfe da ke cikin jiki, baya ga narkar da ƙwayoyin ferritin da juyawar jijiyoyin, waɗanda ke da alaƙa da ajiya da safarar baƙin ƙarfe a cikin jiki.

Bugu da kari, ana iya ba da umarnin wasu gwaje-gwajen don taimakawa wajen bincika musabbabin cutar hemochromatosis, kuma ana iya ba da shawarar mai zuwa:

  • Gwajin kwayoyin halitta, wanda na iya nuna canje-canje a cikin kwayoyin halittar da ke haifar da cutar;
  • Kwayar halittar hanta, musamman ma lokacin da har yanzu ba a sami damar tabbatar da cutar ba ko tabbatar da ajiyar baƙin ƙarfe a cikin hanta ba;
  • Gwajin gwajin Phlebotomy, wanda aka yi tare da janyewar jini da sa ido kan matakan ƙarfe, ana nuna shi galibi ga mutanen da ba za su iya shan kwayar cutar hanta ba ko kuma inda har yanzu akwai shakku game da ganewar;

Har ila yau masanin lafiyar zai iya neman auna matakan enzymes na hanta, gudanar da bincike kan aiki ko ajiyar baƙin ƙarfe a cikin gabobin da za a iya shafa, tare da ware wasu cututtukan da ka iya haifar da irin wannan alamun.


Hemochromatosis ya kamata a bincika a cikin mutanen da ke da alamun bayyanar, lokacin da cutar hanta da ba a bayyana ba, ciwon sukari, cututtukan zuciya, lalatawar jima'i ko cututtukan haɗin gwiwa, da kuma mutanen da ke da dangi na farko da ke fama da cutar ko waɗanda ke da canje-canje a cikin yawan jini yana gwada baƙin ƙarfe.

Dalilin cutar hemochromatosis

Hemochromatosis na iya faruwa sakamakon canjin kwayoyin halitta ko sakamakon cututtukan da suka shafi lalata jajayen ƙwayoyin jini, wanda ke inganta sakin ƙarfe a cikin jini. Don haka, gwargwadon sanadin, ana iya rarraba hemochromatosis zuwa:

  • Hemochromatosis na gado, cewa shine babban dalilin cutar kuma hakan yana faruwa ne sakamakon maye gurbi da kwayoyin halittar dake dauke da sinadarin iron a bangaren narkewa, wanda zai fara sha da yawa, yana kara yawan karfen da ke zagayawa a cikin kwayoyin halitta;
  • Secondary ko samu haemochromatosis, wanda tarin ƙarfe ke faruwa a cikinsa saboda wasu yanayi, galibi hemoglobinopathies, wanda lalata jajayen ƙwayoyin jini ke fitar da baƙin ƙarfe mai yawa a cikin jini. Sauran dalilan su ne karin jini, ciwan mara lokaci ko amfani da magungunan anemia, misali.

Yana da mahimmanci cewa likita ya gano dalilin cutar hemochromatosis, saboda haka yana yiwuwa a nuna mafi dacewa magani, yana taimakawa wajen hana rikice-rikice da sauƙaƙe alamun da ke haifar da ƙarfe mai yawa.


Yadda ake yin maganin

Maganin hemochromatosis ba shi da magani, duk da haka, ana iya yin magani a matsayin hanya don rage baƙin ƙarfe a cikin jini da hana jeri a cikin gabobin. Don haka, a waɗannan yanayin, babban nau'in magani shine phlebotomy, wanda kuma ake kira da zub da jini, wanda ake cire wani ɓangare na jini don baƙin ƙarfe ya zama wani ɓangare na sabbin jajayen ƙwayoyin jini da jiki ke samarwa.

Wannan maganin yana da wani zama na farko mai saurin tashin hankali, amma ya zama dole a yi allurai masu gyara, wanda kusan ana daukar 350 zuwa 450 ml na jini sau 1 zuwa 2 a sati. Bayan haka, ana iya zama zama tazara bisa ga sakamakon binciken da aka biyo baya, wanda likitan jini ya nuna.

Wata hanyar magani ita ce ta amfani da magungunan da aka sani da masu goge baƙin ƙarfe ko "masu satar abubuwa", kamar su Desferroxamine, yayin da suke inganta rage tasirin ƙarfe da ke zagawa. Wannan magani ana nuna shi ga mutanen da ba za su iya jure wa phlebotomy ba, musamman waɗanda ke fama da matsanancin ƙarancin jini, ciwon zuciya ko ciwan hanta mai saurin ci gaba.

Duba ƙarin cikakkun bayanai game da maganin ƙarfe mai yawa a cikin jini.

Yaya ya kamata abincin ya kasance

Baya ga maganin da likita ya nuna, yana da mahimmanci a kula da abinci, kuma ana ba da shawarar a guji yawan cin abinci mai wadataccen ƙarfe. Wasu jagororin da suka danganci abinci sune:

  • Guji cin nama a cikin adadi mai yawa, yana fifita farin nama;
  • Ku ci kifi a kalla sau biyu a mako;
  • Guji cin kayan lambu masu wadataccen ƙarfe, kamar alayyafo, gwoza ko koren wake, fiye da sau ɗaya a mako;
  • Ku ci cikakkiyar gurasar alkama maimakon farin ko wadataccen burodi;
  • Ku ci cuku, madara ko yogurt yau da kullun saboda alli yana rage karfin ƙarfe;
  • Guji cin busassun drya ,an itace, kamar su zabibi, da yawa saboda yana da wadatar ƙarfe.

Bugu da kari, ya kamata mutum ya guji abubuwan sha na giya domin kauce wa lalacewar hanta kuma kada ya sha sinadarin bitamin da sinadarin iron da bitamin C, saboda wannan yana kara ƙarfe ƙarfen.

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