Lambert-Eaton Ciwon Cutar Myasthenic

Wadatacce

• Menene alamun cutar Lambert-Eaton Myasthenic Syndrome?
• Menene ke haifar da Lambert-Eaton Myasthenic Syndrome?
• Bincikowa Lambert-Eaton Myasthenic Syndrome
• Kula da Lambert-Eaton Ciwon Cutar Myasthenic
• Menene hangen nesa?

Menene Lambert-Eaton Ciwon Cutar Myasthenic?

Lambert-Eaton myasthenic syndrome (LEMS) cuta ce mai saurin kamuwa da cutar kansa wanda ke shafar ikonka na motsawa. Tsarin ku na rigakafi kan tsoka wanda ke haifar da wahalar tafiya da sauran matsalolin murdedeji.

Ba za a iya warkar da cutar ba, amma alamun na iya ragewa na ɗan lokaci idan ka yi ƙoƙari. Kuna iya sarrafa yanayin tare da magani.

Menene alamun cutar Lambert-Eaton Myasthenic Syndrome?

Babban alamun LEMS sune raunin kafa da wahalar tafiya. Yayin da cutar ta ci gaba, za ku kuma fuskanci:

• rauni a cikin tsokoki na fuska
• alamun cutar tsoka
• maƙarƙashiya
• bushe baki
• rashin ƙarfi
• matsalolin mafitsara

Rashin rauni na kafa yakan inganta na ɗan lokaci akan aiki. Yayinda kuke motsa jiki, acetylcholine yana ginawa cikin adadi mai yawa don ba da ƙarfi ƙarfi don inganta cikin ɗan gajeren lokaci.

Akwai rikitarwa da yawa waɗanda ke da alaƙa da LEMS. Wadannan sun hada da:

• matsalar numfashi da haɗiyewa
• cututtuka
• raunin da ya faru saboda faɗuwa ko matsaloli tare da daidaito

Menene ke haifar da Lambert-Eaton Myasthenic Syndrome?

A cikin wata cuta ta cikin jiki, tsarin garkuwar jikinku yayi kuskure ga jikinku don baƙon abu. Tsarin ku na rigakafi yana samar da ƙwayoyin cuta waɗanda ke kai hari ga jikinku.

A cikin LEMS, jikinku yana kaiwa ƙarshen jijiyoyin da ke kula da adadin fitowar acetylcholineyour ɗinku. Acetylcholine mai kwakwalwa ne wanda ke haifar da raunin tsoka. Mutuwar tsoka yana ba ka damar yin motsi na son rai kamar tafiya, motsa yatsunku, da kuma daga kafaɗunku.

Musamman, jikinka yana kai hari ga furotin da ake kira tashar wutar lantarki mai ƙarancin ƙarfi (VGCC). Ana buƙatar VGCC don sakin acetylcholine. Ba kwa samar da isasshen acetylcholine lokacin da aka afkawa VGCC, don haka tsokoki naku basu iya aiki da kyau ba.

Yawancin lamura na LEMS suna da alaƙa da cutar huhu. Masu bincike sunyi imanin cewa kwayoyin cutar kansa suna samar da furotin na VGCC. Wannan yana haifar da garkuwar jikinku don yin rigakafi akan VGCC. Wadannan kwayoyi masu kare jiki daga nan sai su afkawa kwayoyin cutar kansa da na tsoka. Kowa na iya haɓaka LEMS a rayuwarsu, amma cutar sankarar huhu na iya haɓaka haɗarin haɓaka yanayin. Idan akwai tarihin cututtukan autoimmune a cikin danginku, kuna iya kasancewa cikin haɗarin haɓaka LEMS.

Bincikowa Lambert-Eaton Myasthenic Syndrome

Don bincika LEMS, likitanku zai ɗauki cikakken tarihi kuma yayi gwajin jiki. Kwararka zai nemi:

• raguwar hankali
• asarar tsoka
• rauni ko matsala motsi wanda ya sami mafi kyau tare da aiki

Likitanku na iya yin odar gwaje-gwaje da yawa don tabbatar da yanayin. Gwajin jini zai nemi ƙwayoyin cuta akan VGCC (anti-VGCC antibodies). Hanyoyin lantarki (EMG) yana gwada ƙwayoyin tsoka ta hanyar ganin yadda suke aikatawa yayin motsa su. An saka ƙaramin allura a cikin tsoka kuma an haɗa shi zuwa mita. Za a umarce ku da ku kulla wannan tsoka, kuma mita zai karanta yadda tsoffinku suka amsa.

Wani gwajin da za'a iya yi shine gwajin saurin tafiyar karfin jijiyoyin jiki (NCV). Don wannan gwajin, likitanka zai sanya wayoyi a saman fatarka wanda zai rufe babbar tsoka. Facin yana ba da siginar lantarki wanda ke motsa jijiyoyi da tsoka. Aikin da ya samo asali daga jijiyoyi an ɗauke shi ta wasu wayoyi kuma ana amfani dashi don gano yadda saurin jijiyoyin suka amsa ga motsa jiki.

Kula da Lambert-Eaton Ciwon Cutar Myasthenic

Ba za a iya warkar da wannan yanayin ba. Za ku yi aiki tare da likitanku don gudanar da duk wasu yanayi, kamar su sankarar huhu.

Kwararka na iya bayar da shawarar maganin immunoglobulin (IVIG) na cikin jini. Don wannan maganin, likitanka zaiyi allurar wani mawuyacin mahimmanci wanda zai kwantar da tsarin garkuwar jiki. Wani magani mai yiwuwa shine plasmapheresis. Ana cire jini daga jiki, kuma ana raba ruwan jini. Ana cire kwayoyin cutar, kuma an mayar da jini a jiki.

Magunguna waɗanda ke aiki tare da tsarin murdede ku na iya sauƙaƙe alamun bayyanar wani lokaci. Wadannan sun hada da mestinon (pyridostigmine) da 3, 4 diaminopyridine (3, 4-DAP).

Wadannan magunguna suna da wahalar samu, kuma ya kamata kayi magana da likitanka dan neman karin bayani.

Menene hangen nesa?

Kwayar cututtukan na iya inganta ta hanyar kula da wasu larurorin, danne tsarin garkuwar jiki, ko cire kwayoyin cuta daga jini. Ba kowa ya amsa da kyau ga magani ba. Yi aiki tare da likitanka don fito da tsarin maganin da ya dace.