Paramyloidosis: menene kuma menene alamun

Wadatacce

• Menene alamun
• Matsaloli da ka iya haddasawa
• Yadda ake yin maganin

Paramyloidosis, wanda kuma ake kira cututtukan ƙafa ko Familial Amyloidotic Polyneuropathy, cuta ce mai saurin gaske wacce ba ta da magani, na asalin kwayar halitta, wanda ke nuni da samar da zaren amyloid ta hanta, wanda aka ajiye shi a cikin kyallen takarda da jijiyoyi, yana lalata su a hankali.

Wannan cuta ana kiranta da cutar ƙafa saboda a ƙafafun ne alamun ke bayyana a karon farko kuma, da kaɗan kaɗan, sukan bayyana a wasu yankuna na jiki.

A cikin paramyloidosis, rashin jijiyoyin jijiyoyin jiki suna haifar da yankunan da waɗannan jijiyoyin suka mamaye, abin da ke haifar da canje-canje a cikin ƙwarewar zafi, sanyi, zafi, taɓawa da faɗakarwa. Bugu da kari, karfin motsa jiki ya shafi kuma jijiyoyin sun rasa karfin tsokarsu, suna fama da tsananin atrophy da asarar ƙarfi, wanda ke haifar da wahala wajen tafiya da amfani da gaɓoɓi.

Menene alamun

Paramyloidosis yana shafar tsarin jijiyoyin jiki, yana haifar da fitowar:

• Matsalar zuciya, kamar ƙaran jini, arrhythmias da toshewar atrioventricular;
• Maganin rashin karfin jiki;
• Matsalolin hanji, kamar su maƙarƙashiya, gudawa, rashin saurin fitsari da tashin zuciya da amai, saboda wahalar shigar ciki;
• Rashin aikin fitsari, kamar riƙe fitsari da rashin nutsuwa da canje-canje a cikin matakan tacewar duniya;
• Rashin lafiyar ido, irin su lalacewar ɗalibai da makanta.

Bugu da kari, a matakin karshe na cutar, mutum na iya fama da raunin motsi, yana buƙatar keken hannu ko zama a gado.

Cutar galibi tana bayyana tsakanin shekaru 20 zuwa 40, wanda ke haifar da mutuwa shekaru 10 zuwa 15 bayan fara alamun farko.

Matsaloli da ka iya haddasawa

Paramyloidosis wata cuta ce ta gado wacce ba ta da magani kuma ba ta da magani kuma hakan ya samo asali ne daga canjin kwayar halitta a cikin furotin na TTR, wanda ya kunshi sanyawa a cikin kyallen takarda da jijiyoyin wani abu na fibrillar da hanta ya samar, wanda ake kira amyloid.

Bayyanar wannan abu a cikin kyallen takarda yana haifar da raguwar ci gaba a cikin laushin hali da karfin motsa jiki.

Yadda ake yin maganin

Magani mafi inganci ga paramyloidosis shine dasawar hanta, wanda ke iya dakushe ci gaban cutar dan kadan. Ana nuna amfani da magungunan rigakafin rigakafi don hana jikin mutum ƙi ƙi da sabon sashin jiki, amma sakamakon illa mara kyau na iya tashi.

Bugu da kari, likita na iya bayar da shawarar wani magani, tare da sunan Tafamidis, wanda ke taimakawa jinkirin ci gaban cutar.