Mawallafi: Clyde Lopez
Ranar Halitta: 23 Yuli 2021
Sabuntawa: 21 Yuni 2024
Anonim
IgA cutar vasculitis - Henoch-Schönlein purpura - Magani
IgA cutar vasculitis - Henoch-Schönlein purpura - Magani

IgA vasculitis cuta ce da ke tattare da launuka masu shunayya akan fata, ciwon haɗin gwiwa, matsalolin hanji, da kuma glomerulonephritis (wani nau'in cutar koda) An kuma san shi da suna Henoch-Schönlein purpura (HSP).

IgA vasculitis yana faruwa ne ta hanyar mawuyacin martani na tsarin garkuwar jiki. Sakamakon shine kumburi a cikin jijiyoyin microscopic na jini a cikin fata. Hakanan ana iya shafar jijiyoyin jini a gidajen abinci, koda, ko hanji. Babu tabbacin dalilin da ya sa hakan ke faruwa.

Cutar ciwo galibi ana ganin ta tsakanin yara tsakanin shekaru 3 zuwa 15, amma ana iya ganin ta cikin manya. Ya fi faruwa ga yara maza fiye da na mata. Mutane da yawa da suka kamu da wannan cuta suna da cutar numfashi ta sama a cikin makonnin da suka gabata.

Kwayar cututtuka da fasalin IgA vasculitis na iya haɗawa da:

  • Dodan shuni masu launin fata (purpura). Wannan yana faruwa kusan kusan yara tare da yanayin. Wannan galibi yana faruwa ne a kan gindi, ƙananan ƙafafu, da gwiwar hannu.
  • Ciwon ciki.
  • Hadin gwiwa.
  • Fitsari mara kyau (mai yiwuwa ba shi da wata alama).
  • Gudawa, wani lokacin na jini.
  • Hive ko angioedema.
  • Tashin zuciya da amai.
  • Kumburi da zafi a cikin mahaifa na yara maza.
  • Ciwon kai.

Mai ba da lafiyar zai kalli jikinku ya kalli fatarku. Jarabawar jiki za ta nuna ciwon fata (purpura, raunuka) da haɗin gwiwa.


Gwaje-gwaje na iya haɗawa da:

  • Yin fitsari ya kamata a yi a kowane hali.
  • Kammala lissafin jini. Platelet din na iya zama na al'ada.
  • Gwajin coagulation: waɗannan ya zama al'ada.
  • Biopsy na fata, musamman ma a cikin manya.
  • Gwajin jini don neman wasu abubuwan da ke haifar da kumburin jijiyoyin jini, kamar su lupus erythematosus na tsari, cutar haɗarin cutar ANCA ko ciwon hanta.
  • A cikin manya, ya kamata a yi biopsy na koda.
  • Gwajin hoto na ciki idan ciwo ya kasance.

Babu takamaiman magani. Yawancin lamura suna tafiya da kansu. Hadin gwiwa yana iya inganta tare da NSAIDs kamar naproxen. Idan alamomi basu gushe ba, za'a iya rubuta muku maganin corticosteroid kamar prednisone.

Cutar ta fi samun sauki da kanta. Kashi biyu bisa uku na yara masu fama da cutar IgA vasculitis suna da kashi ɗaya ne kawai. Daya bisa uku na yara suna da ƙarin aukuwa. Yakamata mutane su sami bin likita na kusa na tsawon watanni 6 bayan abubuwan da suka faru don neman alamun cutar koda. Manya suna da haɗarin kamuwa da cutar koda mai tsanani.


Matsaloli na iya haɗawa da:

  • Zuban jini a cikin jiki
  • Toshe hanji (a cikin yara)
  • Matsalar koda (a wasu lokuta)

Kira mai ba da sabis idan:

  • Kuna ci gaba bayyanar cututtukan IgA vasculitis, kuma suna ƙarewa fiye da 'yan kwanaki.
  • Kuna da fitsari mai launi ko ƙarancin fitsari bayan faruwar lamarin.

Immunoglobulin A vasculitis; Leukocytoclastic vasculitis; Henoch-Schönlein purpura; HSP

  • Henoch-Schonlein purpura a ƙasan ƙafafu
  • Henoch-Schonlein purpura
  • Henoch-Schonlein purpura
  • Henoch-Schonlein purpura
  • Henoch-Schonlein purpura akan kafar jariri
  • Henoch-Schonlein purpura akan kafafun jariri
  • Henoch-Schonlein purpura akan kafafun jariri
  • Henoch-Schonlein purpura akan kafafu

Arntfield RT, Hicks CM. Tsarin lupus erythematosus da maganin vasculitides. A cikin: Walls RM, Hockberger RS, Gausche-Hill M, eds. Magungunan gaggawa na Rosen: Ka'idoji da Aikin Gwajin Asibiti. 9th ed. Philadelphia, PA: Elsevier; 2018: babi 108.


Dinulos JGH. Rawanin tabin hankali da cutar vasculitis. A cikin: Habif TP, Dinulos JGH, Chapman MS, Zug KA, eds. Ciwon Fata: Ganewar asali da Jiyya. 4th ed. Philadelphia, PA: Elsevier; 2018: babi na 11.

Feehally J, FLoege J. Immunoglobulin A nephropathy da IgA vasculitis (Henoch-Schönlein purpura). A cikin: Feehally J, Floege J, Tonelli M, Johnson RJ, eds. M Clinical Nephrology. Na 6 ed. Philadelphia, PA: Elsevier; 2019: babi na 23.

Hahn D, Hodson EM, Willis NS, Craig JC. Sanarwa don hanawa da magance cutar koda a cikin Henoch-Schönlein purpura (HSP). Cochrane Database Syst Rev.. 2015; (8): CD005128. PMID: 26258874 www.ncbi.nlm.nih.gov/pubmed/ 26258874.

Lu S, Liu D, Xiao J, et al. Kwatanta tsakanin manya da yara tare da Henoch-Schönlein purpura nephritis. Pediatr Nephrol. 2015; 30 (5): 791-796. PMID: 25481021 www.ncbi.nlm.nih.gov/pubmed/25481021.

Patterson JW. Tsarin yanayin vasculopathic. A cikin: Patterson JW, ed. Ilimin Lafiyar Weedon. 4th ed. Philadelphia, PA: Elsevier Churchill Livingstone; 2016: babi na 8.

Sunderkötter CH, Zelger B, Chen KR, et al. Nomenclature na cutanous vasculitis: marawar dermatologic zuwa revaddamarwar Taron Internationalasashen Duniya na pasashen Chapel Hill na 2012 wanda aka gyara Arthritis Rheumatol. 2018; 70 (2): 171-184. PMID: 29136340 www.ncbi.nlm.nih.gov/pubmed/29136340.

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