Ciwan jini

Hemophilia yana nufin rukuni na rikicewar jini wanda ɗaukar jini yana ɗaukar lokaci mai tsawo.

Akwai hanyoyi biyu na hemophilia:

• Hemophilia A (gargajiya hemophilia, ko factor VIII rashi)
• Hemophilia B (cutar Kirsimeti, ko rashi IX)

Lokacin da kuka zub da jini, jerin maganganu na faruwa a cikin jiki wanda ke taimakawa yaduwar jini. Wannan tsari shi ake kira coagulation cascade. Ya ƙunshi sunadarai na musamman da ake kira coagulation, ko abubuwan da ke haifar da daskarewa. Kuna iya samun dama mafi girma na zub da jini idan ɗayan ko fiye daga waɗannan abubuwan sun ɓace ko basa aiki kamar yadda ya kamata.

Hemophilia yana faruwa ne sakamakon rashin daskarewar jini VIII ko IX a cikin jini. A mafi yawan lokuta, hemophilia ana ratsa ta cikin dangi (wadanda aka gada). Yawancin lokaci, ana ba da shi ga yara maza.

Babban alamun cutar hemophilia shine zubar jini. Ba za a iya gano lokuta masu sauƙi ba har sai daga baya a rayuwa, bayan zubar jini da yawa bayan tiyata ko rauni.

A cikin mafi munin yanayi, zubar jini na faruwa ba tare da wani dalili ba. Zubar da jini na ciki na iya faruwa a ko'ina kuma zubar jini cikin haɗin gwiwa abu ne na yau da kullun.

Mafi yawan lokuta, ana gano hemophilia bayan mutum yana da matsalar zubar jini mara kyau. Hakanan za'a iya bincikar shi ta hanyar gwajin jini da aka yi don gano matsalar, idan sauran yan uwa suna da yanayin.

Maganin da ya fi dacewa shi ne maye gurbin abin da ya ɓata jini a cikin jini ta jijiya (infusions intravenous).

Ana buƙatar kulawa ta musamman yayin aikin tiyata idan kuna da wannan cuta ta zubar jini. Don haka, tabbatar cewa ka gaya wa likitanka cewa kana da wannan matsalar.

Hakanan yana da matukar mahimmanci raba bayanai game da cutar ku ga danginku na jini domin suma zasu iya shafa.

Kasancewa cikin ƙungiyar tallafi inda membobinta ke raba batutuwan yau da kullun na iya sauƙaƙa damuwar wata cuta mai ɗorewa (mai ɗorewa).

Yawancin mutane masu cutar hemophilia suna iya yin al'amuran yau da kullun. Amma wasu mutane suna zub da jini a cikin mahaɗin, wanda zai iya iyakance ayyukansu.

Wasu yan tsirarun mutane masu cutar hemophilia na iya mutuwa saboda tsananin zubar jini.

Ciwan jini A; Classic hemophilia; Dalilin karancin VIII; Ciwon jini B; Cutar Kirsimeti; Dalilin IX rashi; Rashin jini - hemophilia

• Jinin jini

Carcao M, Moorehead P, Lillicrap D. Hemophilia A da B. A cikin: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Ka'idoji da Aiki. 7th ed. Philadelphia, PA: Elsevier; 2018: babi na 135.

Zauren JE. Hemostasis da jinin jini. A cikin: Hall JE, ed. Guyton da Hall Littafin Littattafan Jiki. 13th ed. Philadelphia, PA: Elsevier; 2016: babi na 37.

Ragni MV. Cutar rashin jini: nakasar rashin ciwan coagulation. A cikin: Goldman L, Schafer AI, eds. Magungunan Goldman-Cecil. 25th ed. Philadelphia, PA: Elsevier Saunders; 2016: babi na 174.