Mawallafi: Virginia Floyd
Ranar Halitta: 12 Agusta 2021
Sabuntawa: 22 Yuni 2024
Anonim
How von Willebrand Factor and ADAMTS13 Regulate Clotting
Video: How von Willebrand Factor and ADAMTS13 Regulate Clotting

Von Willebrand cuta ita ce cuta mafi yawan jini da ake gado.

Von Willebrand cuta yana haifar da ƙarancin factor von Willebrand. Yanayin Von Willebrand yana taimakawa platelets jini su dunkule wuri ɗaya kuma su manne a bangon jijiyoyin jini, wanda ya zama dole don ciwan jini na yau da kullun. Akwai nau'ikan cutar von Willebrand.

Tarihin dangi game da cutar zubar jini shine asalin haɗarin.

Kwayar cutar na iya haɗawa da:

  • Jinin al'ada na al'ada
  • Zubar da jini daga gumis
  • Isingaramar
  • Hancin Hanci
  • Rushewar fata

Lura: Yawancin mata masu fama da jinni mai ɗari ko na tsawan lokaci ba su da cutar von Willebrand.

Von Willebrand cuta na iya zama da wuyar ganewa. Matakan ƙananan abubuwan Willebrand da zubar jini ba koyaushe ke nuna cewa kuna da cutar von Willebrand ba.

Gwajin da za a iya yi don gano wannan cutar sun haɗa da:

  • Lokacin zuban jini
  • Rubuta jini
  • Matakan VIII
  • Nazarin aikin platelet
  • Countididdigar platelet
  • Ristocetin gwajin gwagwarmaya
  • Von Willebrand factor takamaiman gwaje-gwaje

Jiyya na iya haɗawa da DDAVP (desamino-8-arginine vasopressin). Magani ne don haɓaka matakin matakin von Willebrand kuma rage damar zuban jini.


Koyaya, DDAVP baya aiki don kowane nau'in cutar von Willebrand. Yakamata ayi gwaji don tantance wane irin von Willebrand kuke dashi. Idan za a yi muku tiyata, likitanku na iya ba ku DDAVP kafin a yi muku tiyata don ganin idan matakan abubuwan von Willebrand sun ƙaru.

Magungunan Alphanate (antihemophilic factor) an yarda su rage zub da jini a cikin mutanen da ke fama da cutar waɗanda dole ne su sami tiyata ko kuma duk wata hanya mai cutarwa.

Hakanan ana iya amfani da plasma ta jini ko wasu abubuwan shirye-shiryen VIII don rage zubar jini.

Zubar jini na iya raguwa yayin daukar ciki. Matan da ke da wannan matsalar galibi ba sa samun yawan jini yayin haihuwa.

Wannan cuta tana yaduwa ne ta hanyar dangi. Bayar da shawara kan kwayar halitta na iya taimaka wa iyaye masu zuwa su fahimci haɗarin ga yaransu.

Zubar jini na iya faruwa bayan tiyata ko kuma lokacin da aka cire haƙori.

Asfirin da sauran cututtukan cututtukan cututtukan ƙwayoyin cuta (NSAIDs) na iya ƙara wannan yanayin. Kada ku ɗauki waɗannan magunguna ba tare da fara magana da mai ba da lafiyarku ba.


Kira wa mai ba ku sabis idan zub da jini ya auku ba tare da dalili ba.

Idan kuna da cutar von Willebrand kuma kuna shirin yin tiyata ko kuma kuna cikin haɗari, tabbatar ku ko danginku sun gaya wa masu samarwa yanayinku.

Rashin jini - von Willebrand

  • Tsarin jini
  • Jinin jini

Ambaliyar VH, Scott JP. Von Willebrand cuta. A cikin: Kliegman RM, St. Geme JW, Blum NJ, Shah SS, Tasker RC, Wilson KM, eds. Nelson Littafin koyar da ilimin yara. 21st ed. Philadelphia, PA: Elsevier; 2020: babi na 504.

James P, Rydz N. Tsarin, ilmin halitta, da jinsin halittar von Willebrand factor. A cikin: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Ka'idoji da Aiki. 7th ed. Philadelphia, PA: Elsevier; 2018: babi na 138.


Neff AT. Von Willebrand cuta da rashin daidaituwa na jini na platelet da aikin jijiyoyin jini. A cikin: Goldman L, Schafer AI, eds. Magungunan Goldman-Cecil. 26th ed. Philadelphia, PA: Elsevier; 2020: babi na 164.

Samuels P. Rikicin Hematologic na ciki. A cikin: Landon MB, Galan HL, Jauniaux ERM et al, eds. Gabbe's Obetetrics: Ciki da Cutar Matsala. 8th ed. Philadelphia, PA: Elsevier; 2021: babi na 49.

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