Glanzmann thrombasthenia

Glanzmann thrombasthenia cuta ce mai saurin yaduwar jini. Platelets wani bangare ne na jini wanda ke taimakawa wajen daskarewar jini.

Glanzmann thrombasthenia yana faruwa ne sakamakon ƙarancin furotin wanda yake yawanci akan platelet. Ana buƙatar wannan sinadarin don platelets su dunƙu wuri ɗaya don samar da daskarewar jini.

Yanayin na haihuwa ne, wanda ke nufin ya kasance daga haihuwa. Akwai rashin daidaito da yawa da ke haifar da yanayin.

Kwayar cutar na iya haɗawa da ɗayan masu zuwa:

• Zubar da jini mai yawa yayin da bayan tiyata
• Danko mai zub da jini
• Bruising a sauƙaƙe
• Zuban jinin haila mai yawa
• Hancin Hancin da baya tsayawa cikin sauki
• Tsawon jini da kananan raunuka

Ana iya amfani da gwaje-gwaje masu zuwa don tantance wannan yanayin:

• Kammala ƙididdigar jini (CBC)
• Gwajin tarin platelet
• Nazarin aikin platelet (PFA)
• Lokacin Prothrombin (PT) da kuma lokacin thromboplastin m (PTT)

Ana iya buƙatar wasu gwaje-gwaje. Yan uwa na iya buƙatar a gwada su.

Babu takamaiman magani don wannan cuta. Ana iya ba da jinin platelet ga mutanen da ke yawan zubar da jini.

Organizationsungiyoyi masu zuwa kyawawan albarkatu ne don bayani game da Glanzmann thrombasthenia:

• Cibiyar Bayar da Bayanan Cututtuka na Halitta da Rare (GARD) - rarediseases.info.nih.gov/diseases/2478/glanzmann-thrombasthenia
• Nationalungiyar forasa don Rare Rashin Lafiya (NORD) - rarediseases.org/rare-diseases/glanzmann-thrombasthenia

Glanzmann thrombasthenia yanayi ne na rayuwa, kuma babu magani. Yakamata ku dau matakai na musamman dan kokarin kaucewa zubar jini idan kuna da wannan matsalar.

Duk wanda ke da cutar zubar jini ya kamata ya guji shan asfirin da sauran kwayoyin cututtukan da ba su shafi kumburi (NSAIDs) kamar su ibuprofen da naproxen. Wadannan kwayoyi na iya tsawan lokutan zub da jini ta hana kwayoyin cutarwa.

Matsaloli na iya haɗawa da:

• Zubar jini mai tsanani
• Karancin karancin karancin karfe a cikin mata masu haila saboda yawan zubar jini mai ban mamaki

Kira mai ba da sabis na kiwon lafiya idan:

• Kuna da zubar jini ko ƙujewar wani dalili da ba a sani ba
• Zubar jini baya tsayawa bayan jiyya da aka saba

Glanzmann thrombasthenia shine yanayin gado. Babu sanannun rigakafin.

Cutar Glanzmann; Thrombasthenia - Glanzmann

Bhatt MD, Ho K, Chan AKC. Rikicin coagulation a cikin jariri. A cikin: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Ka'idoji da Aiki. 7th ed. Philadelphia, PA: Elsevier; 2018: babi na 150.

Nichols WL. Von Willebrand cuta da rashin daidaituwa na jini na platelet da aikin jijiyoyin jini. A cikin: Goldman L, Schafer AI, eds. Magungunan Goldman-Cecil. 25th ed. Philadelphia, PA: Elsevier Saunders; 2016: babi na 173.