Mahara tsarin atrophy - nau'in Parkinsonian
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Nau'in tsarin atrophy- Parkinsonian nau'in (MSA-P) yanayi ne mai wuya wanda ke haifar da alamun bayyanar kama da cutar Parkinson. Koyaya, mutanen da ke tare da MSA-P suna da lalacewar tartsatsi ga ɓangaren tsarin juyayi wanda ke sarrafa mahimman ayyuka kamar bugun zuciya, hawan jini, da zufa.
Sauran nau'in nau'in MSA shine MSA-cerebellar. Ya fi shafar wurare masu zurfi a cikin kwakwalwa, sama da ƙashin baya.
Ba a san dalilin MSA-P ba. Yankunan da abin ya shafa na kwakwalwa sun haɗu tare da wuraren da cutar ta Parkinson ta shafa, tare da alamun bayyanar. Saboda wannan dalili, ana kiran wannan nau'in na MSA parkinsonian.
MSA-P galibi ana gano shi a cikin mazan da suka girmi shekaru 60.
MSA yana lalata tsarin juyayi. Cutar na saurin samun ci gaba cikin sauri. Kimanin rabin mutanen da ke tare da MSA-P sun rasa yawancin ƙwarewar motar su a cikin shekaru 5 da fara cutar.
Kwayar cutar na iya haɗawa da:
- Girgizar ƙasa
- Matsalolin motsi, kamar jinkiri, rashin daidaito, shuffling lokacin tafiya
- Yawan faduwa
- Ciwo da ciwo na jiki (myalgia), da tauri
- Canje-canje na fuska, kamar bayyanar fuska kamar fuska da fuska
- Matsalar tauna ko haɗiye (lokaci-lokaci), ba zai iya rufe bakin ba
- Yanayin bacci mai lalacewa (galibi yayin saurin motsa ido [REM] bacci da dare)
- Jin jiri ko suma yayin tsayawa ko bayan tsayawa tsaye
- Matsalar tashin hankali
- Rashin iko akan hanji ko mafitsara
- Matsaloli tare da aiki wanda ke buƙatar ƙananan motsi (asarar ƙwarewar ƙwarewar motsa jiki), kamar rubutu wanda ƙarami ne kuma mai wahalar karantawa
- Rashin gumi a kowane bangare na jiki
- Rage cikin aikin hankali
- Rashin ciki da matsaloli tare da narkewa
- Matsalolin hali, kamar rashin ƙarfi, sunkuyar da kai, ko durƙushewa
- Gani ya canza, ya rage ko dushe gani
- Canjin murya da magana
Sauran alamun da zasu iya faruwa tare da wannan cuta:
- Rikicewa
- Rashin hankali
- Bacin rai
- Matsalar numfashi da ke da nasaba da bacci, gami da matsalar bacci ko toshewa ta hanyar iska wanda ke haifar da mummunan sauti na jijjiga
Mai ba da lafiyarku zai bincika ku, ya kuma duba idanunku, jijiyoyi, da tsokoki.
Za a ɗauki jininka yayin da kake kwance da tsaye.
Babu takamaiman gwaji don tabbatar da wannan cuta. Likita wanda ya kware a tsarin juyayi (likitan jijiyoyin jiki) na iya yin tantancewar bisa:
- Tarihin bayyanar cututtuka
- Sakamakon binciken jiki
- Yin hukunci da sauran dalilan bayyanar cututtuka
Gwaji don taimakawa tabbatar da ganewar asali na iya haɗawa da:
- MRI na kai
- Matakan norepinephrine na Plasma
- Fitsarin cikin fitsari don norepinephrine kayayyakin lalacewa (fitsari catecholamines)
Babu magani ga MSA-P. Babu wata hanyar da aka sani da za a iya hana cutar ci gaba da munana. Manufar magani ita ce sarrafa alamun.
Ana iya amfani da magungunan ƙwayoyin cuta, kamar su levodopa da carbidopa don rage rawar jiki da wuri ko mara nauyi.
Amma, don mutane da yawa tare da MSA-P, waɗannan magungunan ba sa aiki da kyau.
Za a iya amfani da magunguna don magance ƙananan hawan jini.
Wani na'urar bugun zuciya wanda aka tsara don motsa zuciya don bugawa da sauri (sauri fiye da 100 a kowane minti daya) na iya kara hawan jini ga wasu mutane.
Za a iya magance maƙarƙashiya ta hanyar cin abinci mai ƙwanƙwasa da laxatives. Akwai magunguna don magance matsalolin farji.
Za a iya samun ƙarin bayani da tallafi ga mutanen da ke tare da MSA-P da danginsu a:
- Nationalungiyar forasa don Rare Rashin Lafiya - rarediseases.org/rare-diseases/multiple-system-atrophy
- MSungiyar MSA - www.multiplesystematrophy.org/msa-resources/
Sakamakon MSA ba shi da kyau. Rashin ayyukan tunani da na jiki sannu a hankali yana ƙara muni. Mutuwar farko da alama. Mutane yawanci suna rayuwa shekaru 7 zuwa 9 bayan ganewar asali.
Kira mai ba ku sabis idan kun ci gaba da alamun wannan cuta.
Kira mai ba ku sabis idan an gano ku tare da MSA kuma alamunku sun dawo ko ƙara muni. Hakanan kira idan sababbin bayyanar cututtuka sun bayyana, gami da yiwuwar tasirin magunguna, kamar su:
- Canje-canje a cikin faɗakarwa / hali / yanayi
- Halin yaudara
- Dizziness
- Mafarki
- Movementsungiyoyi marasa son yi
- Rashin aikin tunani
- Tashin zuciya ko amai
- Babban rikicewa ko rikicewa
Idan kana da wani dangi da ke tare da MSA kuma yanayin su ya ragu har ya zama ba za ka iya kula da mutum a gida ba, nemi shawara daga mai ba da dangin ka.
Ciwon Shy-Drager; Neurologic orthostatic hypotension; Ciwon Shy-McGee-Drager; Parkinson da ciwo; MSA-P; MSA-C
Tsarin juyayi na tsakiya da tsarin juyayi na gefe
Fanciulli A, Wenning GK. Mahara-tsarin atrophy. N Engl J Med. 2015; 372 (3): 249-263. PMID: 25587949 pubmed.ncbi.nlm.nih.gov/25587949/.
Jankovic J. Parkinson cuta da sauran rikicewar motsi. A cikin: Daroff RB, Jankovic J, Mazziotta JC, Pomeroy SL, eds. Bradley's Neurology a cikin Clinical Practice. 7th ed. Philadelphia, PA: Elsevier; 2016: babi na 96.
Romero-Ortuno R, Wilson KJ, Hampton JL. Rashin lafiya na tsarin kulawa na kai. A cikin: Fillit HM, Rockwood K, Young J, eds. Littafin karatun Brocklehurst na Magungunan Geriatric da Gerontology. 8th ed. Philadelphia, PA: Elsevier; 2017: babi na 63.