Mawallafi: Marcus Baldwin
Ranar Halitta: 20 Yuni 2021
Sabuntawa: 24 Yuni 2024
Anonim
Tsarin atrophy da yawa - nau'in nau'in cerebellar - Magani
Tsarin atrophy da yawa - nau'in nau'in cerebellar - Magani

Tsarin atrophy da yawa - subtype cerebellar (MSA-C) cuta ce mai saurin gaske wacce ke haifar da yankuna masu zurfi a cikin kwakwalwa, sama da ƙashin baya, don taƙaita MSA-C ada aka san ta da suna olivopontocerebellar atrophy (OPCA).

Ana iya ƙaddamar da MSA-C ta ​​hanyar dangi (hanyar gado). Hakanan yana iya shafar mutane ba tare da sanannen tarihin dangi ba (nau'i-nau'i ba).

Masu binciken sun gano wasu kwayoyin halittar da ke hade da sifar wannan yanayin.

Ba a san dalilin MSA-C a cikin mutane masu sifar ɓarna ba. Cutar sannu a hankali tana yin muni (yana ci gaba).

MSA-C ya ɗan zama sananne a cikin maza fiye da mata. Matsakaicin shekarun farawa shine shekaru 54.

Kwayar cututtukan MSA-C sukan fara ne tun suna ƙarami a cikin mutanen da ke da siffar da aka gada. Babban alamar ita ce damuwa (ataxia) wanda sannu a hankali ke ƙara muni. Hakanan za'a iya samun matsaloli game da daidaitawa, ɓata magana, da wahalar tafiya.

Sauran cututtuka na iya haɗawa da:

  • Motsa ido mara kyau
  • Motsa jiki mara kyau
  • Matsalar hanji ko mafitsara
  • Matsalar haɗiyewa
  • Cold hannuwanku da ƙafa
  • Haskewar kai yayin tsayawa
  • Ciwon kai yayin da yake tsaye hakan yana samun sauki ta wurin kwanciya
  • Clearfin tsoka ko taurin kai, spasms, rawar jiki
  • Lalacewar jijiya (neuropathy)
  • Matsaloli cikin magana da bacci saboda spasms na cordar muryar
  • Matsalolin aikin jima'i
  • Gumi mara kyau

Ana buƙatar cikakken bincike na tsarin likita da na juyayi, gami da nazarin alamomi da tarihin iyali don yin ganewar asali.


Akwai gwaje-gwajen kwayoyin halitta don bincika musabbabin wasu nau'ikan cutar. Amma, babu takamaiman gwaji da ake samu a cikin lamura da yawa. MRI na kwakwalwa na iya nuna canje-canje a cikin girman tsarin kwakwalwar da abin ya shafa, musamman ma yayin da cutar ta ƙara tsananta. Amma yana yiwuwa a sami cuta kuma a sami MRI na al'ada.

Sauran gwaje-gwajen kamar su positron emmo tomography (PET) ƙila za a yi su don hana wasu yanayi. Waɗannan na iya haɗawa da nazarin haɗiye don ganin idan mutum zai iya haɗiye abinci da ruwa.

Babu takamaiman magani ko magani don MSA-C. Manufar ita ce magance alamun da kuma hana rikice-rikice. Wannan na iya haɗawa da:

  • Magunguna masu girgiza, kamar waɗanda ke da cutar Parkinson
  • Jawabin, aikin motsa jiki da na jiki
  • Hanyoyi don hana shake
  • Abubuwan tafiya suna taimakawa don daidaitawa da hana faɗuwa

Groupsungiyoyi masu zuwa na iya ba da albarkatu da tallafi ga mutane tare da MSA-C:

  • Kayar da kawancen MSA - defemsa.org/patient-programs/
  • MSungiyar MSA - www.multiplesystematrophy.org/msa-resources/

MSA-C a hankali yana ƙara muni, kuma babu magani. Kasancewar gaba ɗaya talauci ne. Amma, yana iya zama shekaru kafin wani ya sami rauni sosai.


Matsalolin MSA-C sun haɗa da:

  • Chokewa
  • Kamuwa da cuta daga shaƙar abinci a cikin huhu (mura mai ciwon huhu)
  • Rauni daga faɗuwa
  • Matsalolin abinci mai gina jiki saboda wahalar haɗiyewa

Kira mai ba ku kiwon lafiya idan kuna da alamun bayyanar MSA-C. Kuna buƙatar ganin likitan jijiyoyi. Wannan likita ne wanda ke magance matsalolin tsarin damuwa.

MSA-C; Cerebellar mahara tsarin atrophy; Olivopontocerebellar atrophy; OPCA; Rushewar Olivopontocerebellar

  • Tsarin juyayi na tsakiya da tsarin juyayi na gefe

Ciolli L, Krismer F, Nicoletti F, Wenning GK. Updateaukakawa akan cerearancin cerewararrun nau'ikan atrophy. Cerebellum Ataxias. 2014; 1-14. PMID: 26331038 pubmed.ncbi.nlm.nih.gov/26331038/.

Gilman S, Wenning GK, Low PA, da sauransu. Bayani na yarjejeniya na biyu game da ganewar asali na yawan kwayar cutar. Neurology. 2008; 71 (9): 670-676. PMID: 18725592 pubmed.ncbi.nlm.nih.gov/18725592/.


Jancovic J. Parkinson cuta da sauran rikicewar motsi. A cikin: Daroff RB, Jankovic J, Mazziotta JC, Pomeroy SL, eds. Bradley's Neurology a cikin Clinical Practice. 7th ed. Philadelphia, PA: Elsevier; 2016: babi na 96.

Ma MJ. Kwayar cututtukan ƙwayoyin cuta na cututtukan neurodegenerative a cikin manya. A cikin: Perry A, Brat DJ, eds. Neurowararren urgicalwararren Neurowararren :wararren :abi'a: Hanyar Bincike. 2nd ed. Philadelphia, PA: Elsevier, 2018: babi na 27.

Walsh RR, Krismer F, Galpern WR, et al. Shawarwarin gamsassun tsarin tsarin atrophy na binciken hanyar taswira. Neurology. 2018; 90 (2): 74-82. PMID: 29237794 pubmed.ncbi.nlm.nih.gov/29237794/.

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