Dermatomyositis

Dermatomyositis cuta ce ta tsoka wacce ta shafi kumburi da fatar fata. Polymyositis shine irin wannan yanayin mai kumburi, wanda kuma ya haɗa da rauni na tsoka, kumburi, taushi, da lalacewar nama amma ba fatarar fata. Dukansu ɓangare ne na babban rukuni na cuta da ake kira mai kumburi myopathy.

Dalilin cutar dermatomyositis ba a san shi ba. Masana na ganin hakan na iya faruwa ne sakamakon kamuwa da kwayar cuta ta tsoka ko wata matsala ta garkuwar jiki. Hakanan yana iya faruwa ga mutanen da ke da ciwon daji a ciki, huhu, ko wasu sassan jiki.

Kowa na iya haɓaka wannan yanayin. Mafi yawan lokuta yakan faru ne ga yara yan shekaru 5 zuwa 15 da kuma manya masu shekaru 40 zuwa 60. Yana shafar mata fiye da maza.

Kwayar cutar na iya haɗawa da:

• Raunin tsoka, tauri, ko ciwo
• Matsaloli haɗiyewa
• Launi mai laushi zuwa fatar ido na sama
• Fata mai launin ja mai laushi
• Rashin numfashi

Rashin rauni na tsoka na iya zuwa kwatsam ko ci gaba a hankali tsawon makonni ko watanni. Wataƙila ka sami matsala daga ɗaga hannunka sama da kanka, tashi daga zaune, da hawa matakala.

Fuskar na iya bayyana a fuskarka, wuyan hannu, wuyanka, kafadu, kirji na sama, da baya.

Mai ba da sabis na kiwon lafiya zai yi gwajin jiki. Gwaje-gwaje na iya haɗawa da:

• Gwajin jini don bincika matakan enzymes na tsoka da ake kira creatine phosphokinase da aldolase
• Gwajin jini don cututtukan autoimmune
• ECG
• Kayan lantarki (EMG)
• Hanyoyin fuska ta maganadisu (MRI)
• Gwajin tsoka
• Gwajin fata
• Sauran gwaje-gwajen binciken cutar kansa
• Kirjin x-ray da hoton CT na kirji
• Gwajin aikin huhu
• Nazarin haɗiyewa
• Myositis takamaimai kuma hade autoantibodies

Babban magani shine amfani da magungunan corticosteroid. Yawan maganin a hankali yana narkar dasu yayin da karfin tsoka ya inganta. Wannan yana ɗaukar makonni 4 zuwa 6. Kuna iya tsayawa kan ƙananan kashi na maganin corticosteroid bayan wannan.

Ana iya amfani da magunguna don murƙushe garkuwar jiki don maye gurbin corticosteroids. Wadannan kwayoyi na iya hada da azathioprine, methotrexate ko mycophenolate.

Magungunan da za'a iya gwadawa yayin cutar da ta ci gaba da aiki duk da waɗannan magungunan sune:

• Ciwan gamma globulin
• Kwayoyin halitta

Lokacin da tsokoki suka sami ƙarfi, mai ba ku sabis na iya gaya muku cewa a hankali rage kan allurai. Mutane da yawa da ke cikin wannan yanayin dole ne su sha wani magani da ake kira prednisone har tsawon rayuwarsu.

Idan ciwon daji yana haifar da yanayin, raunin tsoka da kumburi na iya zama mafi kyau yayin da aka cire kumburin.

Kwayar cutar na iya gushewa gaba ɗaya a cikin wasu mutane, kamar yara.

Yanayin na iya zama mummunan ga manya saboda:

• Raunin rauni mai tsanani
• Rashin abinci mai gina jiki
• Namoniya
• Rashin huhu

Babban abin da ke haifar da mutuwa tare da wannan yanayin sune cutar kansa da cutar huhu.

Mutanen da ke da cutar huhu tare da anti-MDA-5 antibody suna da mummunan hangen nesa duk da maganin yanzu.

Matsaloli na iya haɗawa da:

• Cutar huhu
• M gazawar koda
• Ciwon daji (malignancy)
• Kumburin zuciya
• Hadin gwiwa

Kira mai ba ku sabis idan kuna da rauni na tsoka ko wasu alamun alamun wannan yanayin.

• Dermatomyositis - Gottron papule
• Dermatomyositis - Gottron ta papules a hannu
• Dermatomyositis - fatar ido na heliotrope
• Dermatomyositis a kan kafafu
• Dermatomyositis - Gottron papule
• Paronychia - takara
• Dermatomyositis - murjin heliotrope akan fuska

Aggarwal R, Rider LG, Ruperto N, et al. Kwalejin Kwalejin Rheumatology ta Amurka ta 2016 / Leagueungiyar Turai game da Tsarin Rheumatism don imalananan, Matsakaici, da Babban Maganin Magani a Adult Dermatomyositis da Polymyositis: Mungiyar Myositis ta Duniya da Studiesungiyar Nazarin Clinical / ediwararren ediwararren Rwararrun Rwararrun ediwararrun ediwararru ta ediasa. Arthritis Rheumatol. 2017; 69 (5): 898-910. PMID: 28382787 www.ncbi.nlm.nih.gov/pubmed/28382787.

Dalakas MC. Cututtukan tsoka mai kumburi. N Engl J Med. 2015; 373 (4): 393-394. PMID: 26200989 www.ncbi.nlm.nih.gov/pubmed/26200989.

Nagaraju K, Gladue HS, Lundberg IE. Cututtukan kumburi na tsoka da sauran ƙwayoyin cuta. A cikin: Firestein GS, Budd RC, Gabriel SE, McInnes IB, O'Dell JR, eds. Littafin Kelley da Firestein na Rheumatology. 10 ed. Philadelphia, PA: Elsevier; 2017: babi na 85.

Organizationungiyar forasa don Rare Rashin Lafiya yanar gizo. Dermatomyositis. rarediseases.org/rare-diseases/dermatomyositis/. An shiga Afrilu 1, 2019.