Lamellar ichthyosis

Lamellar ichthyosis (LI) wani yanayi ne na fata mara kyau. Ya bayyana a lokacin haihuwa kuma yana ci gaba tsawon rayuwa.

LI shine cututtukan cututtukan jiki. Wannan yana nufin cewa uwa da uba dole ne dukansu su mika kwaya kwaya daya mara kyau ga dan su dan ya kamu da cutar.

Yaran da yawa tare da LI ana haifuwarsu da haske, mai haske, mai laushi mai laushi wanda ake kira membrane na collodion. Saboda wannan dalili, ana kiran waɗannan yara da jariran collodion. Membrane ya zubar a cikin makonni 2 na farko na rayuwa. Fatar da ke ƙarƙashin membrane ja ce kuma mai walƙiya kama da fuskar kifi.

Tare da LI, layin fata na waje wanda ake kira epidermis ba zai iya kare jiki kamar lafiyayyar epidermis ba. A sakamakon haka, jariri mai dauke da LI na iya samun matsalolin lafiya masu zuwa:

• Matsalar ciyarwa
• Rashin ruwa (rashin ruwa)
• Rashin daidaiton ma'adinai a jiki (rashin daidaiton lantarki)
• Matsalar numfashi
• Zafin jiki wanda bai daidaita ba
• Fata ko cututtukan jiki

Yara da manya da LI na iya samun waɗannan alamun:

• Manyan sikeli waɗanda ke rufe yawancin jiki
• Rage ikon yin gumi, yana haifar da yanayin zafi
• Rashin gashi
• Yatattun yatsu da ƙusa
• Fata na tafin hannu da tafin kafa yana kauri

Yaran Collodion yawanci suna buƙatar zama a cikin sashin kulawa mai kulawa da jarirai (NICU). Ana sanya su a cikin babban incubator-zafi. Suna buƙatar ƙarin ciyarwa. Ana bukatar amfani da danshi a fata. Bayan an zubo membrane na collodion, jarirai galibi suna iya komawa gida.

Kulawar fata na tsawon rai ya haɗa da sanya danshin fata don rage kaurin sikeli. Matakan sun hada da:

• Ana amfani da moisturizers zuwa fata
• Magungunan da ake kira retinoids waɗanda ake ɗauka ta baki a cikin mawuyacin hali
• Yanayi mai zafi mai zafi
• Wanka don sassauta sikeli

Yaran suna cikin haɗarin kamuwa da cuta lokacin da suka zubar da membrane na collodion.

Matsalar ido na iya faruwa daga baya a rayuwa saboda idanu ba sa iya rufewa gaba ɗaya.

LI; Collodion jariri - lamellar ichthyosis; Ichthyosis haifuwa; Autosomal recessive congenital ichthyosis - nau'in lamellar ichthyosis

• Ichthyosis, samu - kafafu

Martin KL. Rashin lafiya na keratinization. A cikin: Kliegman RM, St. Geme JW, Blum NJ, Shah SS. Tasker RC, Wilson KM, eds. Nelson Littafin koyar da ilimin yara. 21st ed. Philadelphia, PA: Elsevier; 2020: babi na 677.

Patterson JW. Rashin lafiya na epidermal maturation da keratinization. A cikin: Patterson JW, ed. Ilimin Lafiyar Weedon. 5th ed. Philadelphia, PA: Elsevier; 2021: babi na 10.

Richard G, Ringpfeil F. Ichthyoses, erythrokeratodermas, da rikice-rikice masu alaƙa. A cikin: Bolognia JL, Schaffer JV, Cerroni L, eds. Dermatology. 4th ed. Philadelphia, PA: Elsevier; 2018: babi na 57.