Rashin wadatar fibrinogen

Rashin wadatar fibrinogen wani abu ne mai matukar wuya, rikicewar jini wanda aka gada wanda jini baya yin daskarewa kullum. Yana shafar furotin da ake kira fibrinogen. Ana buƙatar wannan furotin don jini ya daskare.

Wannan cutar ta samo asali ne daga kwayoyin halittu marasa kyau. Fibrinogen ya kamu ne dangane da yadda kwayoyin halittar suka gada:

• Lokacin da kwayar cutar ta mutu ta lalace daga iyaye biyu, mutum zai sami cikakken rashin fibrinogen (afibrinogenemia).
• Lokacin da kwayar cutar da ba ta dace ba ta wuce daga mahaifi daya, mutum zai sami ko dai ya rage matakin fibrinogen (hypofibrinogenemia) ko kuma matsalar aikin fibrinogen (dysfibrinogenemia). Wasu lokuta, waɗannan matsalolin fibrinogen guda biyu na iya faruwa a cikin mutum ɗaya.

Mutanen da ke da cikakken rashin fibrinogen na iya samun ɗayan alamun alamun jini masu zuwa:

• Bruising a sauƙaƙe
• Zuban jini daga igiyar cibiya bayan haihuwa
• Zuban jini a cikin ƙwayoyin mucous
• Zub da jini a cikin kwakwalwa (mai matukar wuya)
• Zuban jini a gidajen abinci
• Zubar da jini mai yawa bayan rauni ko tiyata
• Hancin Hancin da baya tsayawa cikin sauki

Mutanen da ke da ƙananan matakin fibrinogen ba sa yawan zubar jini ba sau da yawa kuma zub da jini ba shi da ƙarfi sosai. Wadanda ke da matsala tare da aikin fibrinogen galibi ba su da alamomi.

Idan mai kula da lafiyarku ya yi zargin wannan matsalar, za ku yi gwaje-gwajen gwaje-gwaje don tabbatar da nau'in cutawar.

Gwajin sun hada da:

• Lokacin zuban jini
• Gwajin Fibrinogen da lokaci mai rarrafe don bincika matakin fibrin da inganci
• Lokaci na thromboplastin (PTT)
• Lokacin Prothrombin (PT)
• Lokacin Thrombin

Za'a iya amfani da wadannan magungunan don lokutan zubar jini ko shirya tiyata:

• Cryoprecipitate (samfurin jini wanda ya ƙunshi ƙwaƙƙwarar fibrinogen da sauran abubuwan haɓaka)
• Fibrinogen (RiaSTAP)
• Plasma (sashin ruwa na jini dauke da abubuwan daskarewa)

Mutanen da ke da wannan yanayin ya kamata su sami rigakafin cutar hepatitis B Yin ƙarin jini da yawa yana ƙara haɗarin kamuwa da cutar hanta.

Yawan zubar jini ya zama gama gari tare da wannan yanayin. Wadannan aukuwa na iya zama mai tsanani, ko ma m. Zubar da jini a cikin kwakwalwa shine babban abin da ke haifar da mutuwa ga mutanen da ke fama da wannan cuta.

Matsaloli na iya haɗawa da:

• Jinin jini tare da magani
• Ci gaban ƙwayoyin cuta (masu hanawa) zuwa fibrinogen tare da magani
• Zuban jini na ciki
• Zubewar ciki
• Rushewar mahaifa
• Sannu a hankali warkar da raunuka

Kirawo mai baka sabis ko ka nemi kulawa ta gaggawa idan kana yawan zubar jini.

Faɗa wa likitanka kafin a yi maka tiyata idan ka sani ko kuma ka yi tsammanin kana da cutar rashin jini.

Wannan yanayin gado ne. Babu sanannun rigakafin.

Afibrinogenemia; Hypofibrinogenemia; Dysfibrinogenemia; Dalilin I rashi

Gailani D, Wheeler AP, Neff AT. Rare coagulation factor ƙarancin. A cikin: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Ka'idoji da Aiki. 7th ed. Philadelphia, PA: Elsevier; 2018: babi na 137.

Ragni MV. Cutar rashin jini: nakasar rashin ciwan coagulation. A cikin: Goldman L, Schafer AI, eds. Magungunan Goldman-Cecil. 25th ed. Philadelphia, PA: Elsevier Saunders; 2016: babi na 174.