Mawallafi: Clyde Lopez
Ranar Halitta: 18 Yuli 2021
Sabuntawa: 1 Yuli 2024
Anonim
03/19/2019 Idiopathic Pulmonary Fibrosis
Video: 03/19/2019 Idiopathic Pulmonary Fibrosis

Idiopathic huhu fibrosis (IPF) yana tabo ko kaurin huhu ba tare da sanannen sanadi ba.

Masu ba da kiwon lafiya ba su san abin da ke haifar da IPF ko me ya sa wasu mutane ke haɓaka shi ba. Idiopathic yana nufin ba a san dalilin ba. Yanayin na iya zama saboda huhu yana amsawa ga wani abu da ba a sani ba ko rauni. Kwayar halitta na iya taka rawa wajen bunkasa IPF. Cutar na faruwa ne galibi a tsakanin mutane tsakanin shekara 60 zuwa 70. IPF ta fi zama ruwan dare a cikin maza fiye da mata.

Lokacin da kake da IPF, huhunka ya zama ya yi tauri kuma ya taurare. Wannan yana sanya wahalar numfashi a gare ka. A cikin mafi yawan mutane, IPF tana ƙara lalacewa da sauri cikin watanni ko overan shekaru. A wasu, IPF ya kara lalacewa a cikin lokaci mai tsawo.

Kwayar cutar na iya haɗawa da ɗayan masu zuwa:

  • Ciwon kirji (wani lokacin)
  • Tari (yawanci bushe)
  • Ba za a iya yin aiki kamar dā ba
  • Ofarancin numfashi yayin aiki (wannan alamar na tsawon watanni ko shekaru, kuma kan lokaci na iya faruwa yayin hutawa)
  • Jin suma
  • Rage nauyi a hankali

Mai ba da sabis ɗin zai yi gwajin jiki kuma ya yi tambaya game da tarihin lafiyar ku. Za a tambaye ku ko kun bayyana ga sinadarin asbestos ko kuma wasu abubuwa masu guba kuma idan kun kasance sigari.


Jarabawar jiki na iya gano cewa kuna da:

  • Murnar numfashi mara kyau da ake kira crackles
  • Fata ta Bluish (cyanosis) a kewayen bakin ko farcen hannu saboda ƙarancin oxygen (tare da cutar mai ci gaba)
  • Fadadawa da lankwasassun kafafun kafa, wanda ake kira kwancen kafa (mai cutar mai ci gaba)

Gwajin da ke taimakawa wajen tantance IPF sun hada da masu zuwa:

  • Bronchoscopy
  • Babban ƙudirin kirji na CT (HRCT)
  • Kirjin x-ray
  • Echocardiogram
  • Matakan matakin oxygen (jinin gas)
  • Gwajin aikin huhu
  • Gwajin tafiya na minti 6
  • Gwaje-gwaje don cututtukan cututtuka irin su cututtukan zuciya na rheumatoid, lupus, ko scleroderma
  • Bude huhu (tiyata) biopsy na huhu

Babu sanannen magani ga IPF.

Ana amfani da jiyya don sauƙaƙe bayyanar cututtuka da rage saurin ci gaban cuta:

  • Pirfenidone (Esbriet) da nintedanib (Ofev) magunguna ne guda biyu waɗanda suke magance IPF. Suna iya taimakawa jinkirin lalacewar huhu.
  • Mutanen da ke da ƙananan iskar oxygen suna buƙatar tallafin oxygen a gida.
  • Gyaran huhu ba zai warkar da cutar ba, amma zai iya taimaka wa mutane motsa jiki da ƙarancin numfashi.

Yin canjin gida da salon rayuwa na iya taimakawa wajen sarrafa alamun numfashi. Idan ku ko kowane dangi kuna shan sigari, yanzu lokaci yayi da za ku daina.


Ana iya yin la'akari da dashen huhu ga wasu mutanen da ke da ci gaban IPF.

Kuna iya sauƙaƙa damuwar rashin lafiya ta shiga ƙungiyar tallafi. Yin tarayya tare da wasu waɗanda suke da masaniya da matsaloli na yau da kullun na iya taimaka muku kada ku ji ku kaɗai.

Ana iya samun ƙarin bayani da tallafi ga mutanen da ke da IPF da dangin su a:

  • Gidajen Fibrosis na Wuta - www.pulmonaryfibrosis.org/life-with-pf/support-groups
  • Lungiyar huhu ta Amurka - www.lung.org/support-and-community/

IPF na iya inganta ko ya kasance mai karko na dogon lokaci tare da ko ba tare da magani ba. Yawancin mutane suna yin muni, koda da magani.

Lokacin da alamun bayyanar numfashi suka zama mafi tsanani, ku da mai ba ku sabis ya kamata ku tattauna maganin da ke tsawanta rayuwa, kamar dashen huhu. Har ila yau tattauna shirin kulawa na gaba.

Matsalolin IPF na iya haɗawa da:

  • Matakan da ba na al'ada ba na jan jinin jini saboda ƙananan matakan oxygen
  • Huhu ya tarwatse
  • Hawan jini a jijiyoyin huhu
  • Rashin numfashi
  • Cor pulmonale (bangaren zuciya na dama-dama)
  • Mutuwa

Kira mai ba da sabis kai tsaye idan kana da ɗayan masu biyowa:


  • Numfashi wanda ya fi wuya, sauri, ko mafi zurfin (ba ku da ikon ɗaukar numfashi)
  • Don jingina gaba lokacin zaune don numfashi cikin nutsuwa
  • Yawan ciwon kai
  • Bacci ko rikicewa
  • Zazzaɓi
  • Muarƙashin duhu lokacin da kuka tari
  • Fingeran yatsan shuɗi ko fatar kewaye da farcen yatsun hannu

Idiopathic yaɗuwa tsakanin kwayar cutar fibrosis ta cikin huhu; IPF; Fibrosis na huhu; Cryptogenic fibrosing alveolitis; CFA; Fibrosing alveolitis; Ciwon pneumonitis na yau da kullun; UIP

  • Yin amfani da oxygen a gida
  • Iarfafawa
  • Klub
  • Tsarin numfashi

Cibiyar Zuciya ta Kasa, huhu, da gidan yanar gizo. Idiopathic huhu fibrosis. www.nhlbi.nih.gov/health-topics/idiopathic-pulmonary-fibrosis. An shiga Janairu 13, 2020.

Raghu G, Martinez FJ. Cutar cututtukan huhu. A cikin: Goldman L, Schafer AI, eds. Magungunan Goldman-Cecil. 26th ed. Philadelphia, PA: Elsevier; 2020: babi na 86.

Raghu G, Rochwerg B, Zhang Y, et al. Aikin ATS / ERS / JRS / ALAT jagorar aikin likita: lura da cutar sankarar iska ta idiopathic. Sabuntawa game da tsarin aikin asibiti na 2011. Am J Respir Masu Kula da Kulawa. 2015; 192 (2): e3-e19. PMID: 26177183 pubmed.ncbi.nlm.nih.gov/26177183/.

Ryu JH, Selman M, Colby TV, King TE. Maganin ciwon mara na idiopathic. A cikin: Broaddus VC, Mason RJ, Ernst JD, et al, eds. Littafin rubutu na Murray da Nadel na Magungunan numfashi. Na 6 ed. Philadelphia, PA: Elsevier Saunders; 2016: babi na 63.

Silhan LL, Danoff SK. Magungunan nonpharmacologic don idiopathic huhu fibrosis. A cikin: Collard HR, Richeldi L, eds. Tsarin Cututtukan Huhu. Philadelphia, PA: Elsevier; 2018: babi na 5.

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