Rashin haƙuri fructose

Rashin haƙuri fructose rashin haƙuri cuta ce wacce mutum ba shi da furotin da ake buƙata don lalata fructose. Fructose shine sukari mai fruita naturallyan itace wanda yake faruwa a hankali cikin jiki. Ana amfani da fructose na mutum a matsayin mai zaki a cikin abinci da yawa, gami da abincin yara da abin sha.

Wannan yanayin yana faruwa ne lokacin da jiki ya rasa wani enzyme da ake kira aldolase B. Ana buƙatar wannan abu don lalata fructose.

Idan mutumin da ba shi da wannan abu ya ci fructose ko sucrose (kara ko sukari mai gwoza, sukari na tebur), canje-canje masu sinadarai masu rikitarwa suna faruwa a jiki. Jiki ba zai iya canza nau'in suga (glycogen) da aka adana cikin glucose ba. A sakamakon haka, sukarin jini yana faduwa kuma abubuwa masu haɗari suna haɗuwa a cikin hanta.

An gaji rashin haƙuri fructose, wanda ke nufin ana iya yada shi ta wurin iyalai. Idan iyaye biyu suna ɗauke da kwafin aiki na aldolase B, ɗayan yaransu suna da damar 25% (1 cikin 4).

Ana iya ganin alamun bayan jariri ya fara cin abinci ko madara.

Alamomin farko na rashin haƙuri na fructose sun yi kama da na galactosemia (rashin iya amfani da sukari galactose). Daga baya alamun cutar sun fi dangantaka da cutar hanta.

Kwayar cutar na iya haɗawa da:

• Vunƙwasawa
• Yawan bacci
• Rashin fushi
• Fata mai launin rawaya ko fararen idanu (jaundice)
• Rashin ciyarwa da ci gaba mara kyau kamar jariri, gazawar bunƙasa
• Matsaloli bayan cin 'ya'yan itatuwa da sauran abincin da ke dauke da fructose ko sucrose
• Amai

Gwajin jiki na iya nuna:

• Liverara hanta da baƙin ciki
• Jaundice

Gwajin da suka tabbatar da cutar sun hada da:

• Gwajin jini
• Gwajin sukarin jini
• Nazarin Enzyme
• Gwajin kwayoyin halitta
• Gwajin aikin koda
• Gwajin aikin hanta
• Gwajin hanta
• Gwajin jini na Uric acid
• Fitsari

Sikarin jini zai zama ƙasa, musamman bayan karɓar fructose ko sucrose. Matakan Uric acid zai zama babba.

Cire fructose da sucrose daga abincin shine magani mai mahimmanci ga yawancin mutane. Ana iya magance matsalolin. Misali, wasu mutane na iya shan magani don rage matakin uric acid a cikin jininsu da rage kasadar su na gout.

Rashin haƙuri fructose na iya zama mai sauƙi ko mai tsanani.

Guji fructose da sucrose yana taimaka wa yawancin yara da wannan yanayin. Hannun hangen nesa yana da kyau a mafi yawan lokuta.

Childrenananan yara da ke da mummunar cutar za su kamu da cutar hanta mai tsanani. Ko cire fructose da sucrose daga abincin bazai hana rigakafin cutar hanta mai ƙarfi cikin waɗannan yara ba.

Yadda mutum yake yi ya dogara da:

• Yaya za'a gano asalin cutar
• Yaya za'a iya cire fructose da sucrose daga abinci
• Ta yaya enzyme yake aiki a jiki

Wadannan rikitarwa na iya faruwa:

• Guji abinci mai ƙunshe da fructose saboda tasirin su
• Zuban jini
• Gout
• Rashin lafiya daga cin abinci mai ɗauke da fructose ko sucrose
• Rashin hanta
• Sugararamar sikari (hypoglycemia)
• Kamawa
• Mutuwa

Kira mai ba da sabis na kiwon lafiya idan ɗanka ya fara bayyanar cututtuka na wannan yanayin bayan fara ciyarwa. Idan yaronka yana da wannan yanayin, masana sun ba da shawarar ganin likita wanda ya ƙware a cikin ƙwayoyin halittar jiki ko kuma kumburi.

Ma'aurata tare da tarihin iyali na rashin haƙuri da fructose waɗanda suke son haihuwa suna iya yin la'akari da shawarwarin kwayoyin halitta.

Yawancin cututtukan cututtukan cutar ana iya kiyaye su ta hanyar rage fructose da sucrose.

Fructosemia; Rashin haƙuri na Fructose; Fructose aldolase B-rashi; Fructose-1, 6-bisphosphate rashi aldolase

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