Dalilin VII rashi

Rashin Factor VII (bakwai) cuta ce ta rashin rashin sunadarin da ake kira factor VII a cikin jini. Yana haifar da matsaloli game da daskarewar jini (coagulation).

Lokacin da kuka zub da jini, jerin maganganu na faruwa a cikin jiki wanda ke taimakawa yaduwar jini. Wannan tsari shi ake kira coagulation cascade. Ya ƙunshi sunadarai na musamman da ake kira coagulation, ko abubuwan da ke haifar da daskarewa. Kuna iya samun damar samun yawan zub da jini idan ɗayan ko fiye daga waɗannan abubuwan sun ɓace ko basa aiki yadda yakamata.

Dalilin VII shine irin wannan tasirin coagulation. Arancin Factor VII yana gudana ne a cikin dangi (wanda aka gada) kuma yana da matukar wuya. Duk iyaye dole ne su sami zuriya don yada cutar ga yaransu. Tarihin dangi game da cutar zubar jini na iya zama haɗarin haɗari.

Arancin Factor VII na iya zama saboda wani yanayin ko amfani da wasu magunguna. Wannan ana kiran sa ƙarancin factor VII rashi. Zai iya faruwa ta hanyar:

• Vitaminarancin bitamin K (ana haihuwar wasu jarirai da rashi bitamin K)
• Ciwon hanta mai tsanani
• Amfani da magunguna wadanda suke hana daskarewa (maganin hana yaduwar jini kamar warfarin)

Kwayar cutar na iya haɗawa da ɗayan masu zuwa:

• Zuban jini daga membran jikinshi
• Zuban jini a cikin gidajen abinci
• Zuban jini cikin tsokoki
• Bruising a sauƙaƙe
• Zuban jinin haila mai yawa
• Hancin Hancin da baya tsayawa cikin sauki
• Zuban jini bayan haihuwa

Gwajin da za a iya yi sun hada da:

• Lokaci na thromboplastin (PTT)
• Plasma factor VII aiki
• Lokacin Prothrombin (PT)
• Nazarin haɗuwa, gwaji na PTT na musamman don tabbatar da rashin ƙarancin VII

Zubar da jini yana iya sarrafawa ta hanyar samun infravenous (IV) infusions na plasma na al'ada, ƙididdigar mahimmancin VII, ko samfurin da aka samar (recombinant) factor VII.

Kuna buƙatar magani mai yawa yayin lokutan zubar jini saboda factor VII baya ɗaukar dogon lokaci a cikin jiki. Hakanan za'a iya amfani da wani nau'i na factor VII da ake kira NovoSeven.

Idan kuna da rashi na VII saboda rashin bitamin K, zaku iya shan wannan bitamin ta baki, ta hanyar allura ƙarƙashin fata, ko ta jijiya (ta jijiyoyin wuya).

Idan kana da wannan cuta ta zub da jini, tabbatar cewa:

• Faɗa wa masu kula da lafiyarku kafin ku sami kowane irin tsari, gami da tiyata da aikin haƙori.
• Faɗa wa danginku saboda suna iya kamuwa da cuta iri ɗaya amma ba su sani ba tukuna.

Waɗannan albarkatun na iya samar da ƙarin bayani game da rashi na Factor VII:

• Gidauniyar Hemophilia ta Kasa: Sauran ficananan Matsaloli - www.hemophilia.org/Bleeding-Disorders/Types-of-Bleeding-Disorders/Other-Factor-Deficiencies
• Nationalungiyar forasa don Rare Rashin Lafiya - rarediseases.org/rare-diseases/factor-vii-deficiency
• NLM Tsarin Gida na Gida - ghr.nlm.nih.gov/condition/factor-vii-deficiency

Kuna iya tsammanin kyakkyawan sakamako tare da magani mai dacewa.

Factorarancin gado VII rashi shine yanayin rayuwa.

Hangen nesa don ƙarancin factor VII rashi ya dogara da dalilin. Idan cutar hanta ce ta haifar da shi, sakamakon ya dogara da yadda za a iya magance cutar hanta. Shan karin bitamin K zai magance karancin bitamin K.

Matsaloli na iya haɗawa da:

• Zub da jini mai yawa (zubar jini)
• Bugun jini ko wasu matsalolin tsarin jijiyoyi daga zubar jini ta tsakiya
• Matsalar haɗin gwiwa a cikin mawuyacin hali lokacin da zub da jini yakan faru sau da yawa

Samo magani na gaggawa yanzunnan idan kuna jinni mai tsanani, mara dalili.

Babu wata sananniyar rigakafi don ƙarancin factor VII rashi. Lokacin da rashin bitamin K ke haifar, amfani da bitamin K na iya taimakawa.

Raunin Proconvertin; Factorarancin ƙarancin abubuwa; Rashin magani mai saurin yaduwar kwayar cuta; Cutar Alexander

• Tsarin jini
• Jinin jini

Gailani D, Wheeler AP, Neff AT. Rare coagulation factor ƙarancin. A cikin: Hoffman R, Benz EJ, Silberstein LE, et al, eds. Hematology: Ka'idoji da Aiki. 7th ed. Philadelphia, PA: Elsevier; 2018: babi na 137.

Zauren JE. Hemostasis da jinin jini. A cikin Hall JE, ed. Guyton da Hall Littafin Littattafan Jiki. 13th ed. Philadelphia, PA: Elsevier; 2016: babi na 37.

Ragni MV. Cutar rashin jini: nakasar rashin ciwan coagulation. A cikin: Goldman L, Schafer AI, eds. Magungunan Goldman-Cecil. 25th ed. Philadelphia, PA: Elsevier Saunders; 2016: babi na 174.