Menene epidermolysis bullosa, cututtuka da magani

Wadatacce

• Babban bayyanar cututtuka
• Dalilin bullous epidermiolysis
• Menene iri
• Yadda ake yin maganin
• Lokacin da ake buƙatar tiyata
• Abin da za a yi don hana bayyanar kumfa
• Yadda ake yin miya
• Menene rikitarwa

Bullous epidermolysis cuta ce ta kwayar halitta wacce ke haifar da samuwar kumfa a jikin fata da kuma sassan jikin mutum, bayan duk wani rikici ko wata karamar damuwa da za ta iya faruwa ta fusatar da tambarin sutura akan fatar ko, a sauƙaƙe, ta cire wani band taimako, misali. Wannan yanayin yana faruwa ne saboda canjin yanayin da ake samu daga iyaye zuwa ga theira childrenansu, wanda ke haifar da canje-canje a cikin yadudduka da abubuwan da ke cikin fata, kamar keratin.

Alamomi da alamomin wannan cutar suna da nasaba da bayyanar wasu ƙuraje masu zafi a fatar da kan kowane ɓangare na jiki, har ma suna iya bayyana a baki, dabino da tafin ƙafa. Wadannan alamun sun banbanta gwargwadon nau'ikan da tsananin epidermolysis bullosa, amma galibi suna samun matsala cikin lokaci.

Jiyya don bullar epidermolysis ya ƙunshi kulawa ta goyan baya, kamar su kiyaye wadataccen abinci mai gina jiki da kuma sanya kumburin fata. Bugu da kari, ana ci gaba da nazari don yin dashen kashin kashi ga mutanen da ke da wannan yanayin.

Babban bayyanar cututtuka

Babban alamun bayyanar cututtukan epidermolysis sune:

• Fushin fata a ƙananan gogayya;
• Bugawa na bayyana a cikin bakin har ma a cikin idanu;
• Warkar da fata tare da kyan gani da fararen fata;
• Nail daidaitawa;
• Gyara gashi;
• Rage gumi ko yawan zufa.

Hakanan ya danganta da tsananin jijiyoyin wuya, raunin yatsu da na yatsu na iya faruwa, wanda ke haifar da nakasa. Duk da kasancewar halayyar bayyanar cututtukan epidermolysis, sauran cututtuka na iya haifar da bayyanar blisters a fata, kamar herpes simplex, epidermolytic ichthyosis, bullous impetigo da pigmentary incontinence. San abin da yake bullous impetigo kuma menene magani.

Dalilin bullous epidermiolysis

Bullous epidermolysis yana faruwa ne ta hanyar maye gurbi da aka watsa daga iyaye zuwa ga yaro, kuma yana iya zama babba, wanda mahaifi daya ke da kwayar cutar, ko recessive, wanda uba da uwa ke ɗauke da kwayar cutar amma babu bayyanar alamu ko alamun cutar cutar.

Yaran da ke da dangi na kusa da cutar ko kuma tare da kwayar cutar ta epidermolysis ana iya haihuwar su da irin wannan yanayin, don haka idan iyaye sun san cewa suna da kwayar cutar ta hanyar gwajin kwayar halitta, ana nuna shawarwarin kwayoyin halitta. Duba menene shawarwar kwayar halitta da yadda ake yinta.

Menene iri

Za'a iya rarraba bullar fashin epidermolysis zuwa nau'i uku ya danganta da layin fatar da ke haifar da ƙura, kamar:

• Bul Sauƙan bayani game da epidermolysis: blistering yana faruwa a saman fata na fata, wanda ake kira epidermis, kuma abu ne gama gari garesu su bayyana a hannaye da ƙafafu. A cikin wannan nau'in yana yiwuwa a ga ƙusoshin ƙusoshin da kuma kauri kuma kumfa ba ya warkewa da sauri;

• Dystrophic epidermolysis bullosa: kumfa a cikin wannan nau'in ya tashi ne saboda lahani a cikin samar da nau'ikan V | I collagen kuma yana faruwa a cikin mafi girman fata na fata, da aka sani da fata;
• Hanyar epidermolysis bullosa: wanda ke tattare da samuwar kumburi saboda kebewar yankin tsakanin matsakaiciyar matsakaiciyar matsakaicin fata kuma a wannan yanayin, cutar tana faruwa ne ta hanyar maye gurbi a cikin kwayoyin halittar da ke hade da fata da epidermis, kamar Laminin 332.

Ciwon kansa na Kindler shima nau'i ne na bullar epidermolysis, amma yana da matukar wuya kuma ya ƙunshi dukkan matakan fata, wanda ke haifar da mummunan rauni. Ba tare da la'akari da nau'in wannan cutar ba, yana da mahimmanci a lura cewa bullous epidermolysis ba ya yaduwa, ma'ana, ba ya wucewa daga mutum ɗaya zuwa wani ta hanyar hulɗa da raunin fata.

Yadda ake yin maganin

Babu takamaiman magani na epidermolysis bullosa, kuma yana da matukar mahimmanci a rinka yin tuntuɓar yau da kullun tare da likitan fata don kimanta yanayin fatar da gujewa matsaloli, kamar su cututtuka, misali.

Maganin wannan cuta ya kunshi matakan tallafi, kamar sanya raunuka da kuma shawo kan zafin kuma, a wasu lokuta, kwantar da asibiti ya zama dole don yin sutturar marainiya, ba tare da ƙwayoyin cuta ba, don haka ana ba da magunguna kai tsaye cikin jijiya, kamar yadda maganin rigakafi a cikin yanayin kamuwa da cuta, da kuma zubar da ƙyallen fata. Koyaya, ana ci gaba da nazarin wasu don aiwatar da dashen ƙwayoyin ƙwayoyin cuta don magance dystrophic bullous epidermolysis.

Ba kamar kumburin da lalacewa ke haifar da konewa ba, blister wanda epidermolysis bullosa ya haifar dole ne a huda shi da takamaiman allura, ta yin amfani da matattarar bakararre, don hana shi yaduwa da haifar da illa ga fata. Bayan zubewa, yana da mahimmanci ayi amfani da samfuri, kamar su fesa antibacterial, don hana cututtuka.

Lokacin da ake buƙatar tiyata

Aikin tiyata na bullous dermatitis galibi ana nuna shi ne don yanayin da tabon da kumfa ya bari ke hana motsa jiki ko haifar da nakasa da ke rage ingancin rayuwa. A wasu lokuta, ana iya amfani da tiyata don sanya fatar jiki, musamman a kan raunuka da ke daukar lokaci mai tsawo don warkewa.

Abin da za a yi don hana bayyanar kumfa

Tunda babu magani, ana yin magani kawai don sauƙaƙe alamomin da rage damar samun sabbin ƙuraje. Mataki na farko shine samun dan kulawa a gida, kamar su:

• Sanya tufafin auduga, guje wa yadudduka na roba;
• Cire alama daga duk tufafi;
• Sanya tufafi juye don kaucewa haɗuwa da na roba da fata;
• Sanya takalmi masu haske kuma masu fadi sosai don sanya katun safa marasa inganci;
• Yi hankali sosai lokacin amfani da tawul bayan wanka, a hankali danna fata tare da tawul mai laushi;
• Aiwatar da Vaseline a yalwace kafin cire suturar kuma kar a tilasta cire ta;
• Idan tufafi daga baya suka makale a fata, bar yankin ya jike cikin ruwa har sai tufafin sun kwance daga fatar ita kadai;
• Rufe raunukan da suturar da ba ta mannawa ba kuma tare da sako-sako na gauze;
• Barci tare da safa da safar hannu don gujewa raunin da ka iya faruwa yayin bacci.

Bugu da kari, idan akwai fata mai kaushi, likita na iya ba da umarnin yin amfani da sinadarin corticosteroids, kamar su prednisone ko hydrocortisone, don magance kumburin fata da rage alamomin, kauce wa yin fatar fata, samar da sabbin lahani. Hakanan ya zama dole a kiyaye yayin wanka, a guji cewa ruwan yayi zafi sosai.

Aikace-aikacen botox a ƙafa yana da alama yana da tasiri wajen hana ƙuƙummawa a cikin wannan yankin, kuma ana nuna ciwon ciki lokacin da ba zai yiwu a ci da kyau ba tare da bayyanar kumburi a cikin baki ko hanji ba.

Yadda ake yin miya

Yin suturar wani bangare ne na aikin wadanda suka kamu da cutar epidermolysis kuma dole ne a sanya wadannan suturar cikin kulawa don hakan zai inganta warkarwa, rage tashin hankali da hana zubar jini daga fata, saboda wannan yana da mahimmanci a yi amfani da samfuran da ba sa jituwa akan fatar , wato, ba su da manne wanda ke haɗawa da ƙarfi sosai.

Don suturar raunuka waɗanda ke da ɓoyayyen ɓoye, yana da muhimmanci a yi amfani da kayan ɗumbin da aka yi da kumfa na polyurethane, yayin da suke shan waɗannan ruwan kuma suna ba da kariya daga ƙananan ƙwayoyin cuta.

A cikin yanayin da raunukan suka riga sun bushe, ana ba da shawarar yin amfani da kayan ado na hydrogel, saboda suna taimakawa kawar da ƙwayar fata da ta mutu da kuma sauƙaƙa zafi, ƙaiƙayi da rashin jin daɗi a yankin. Dole ne a gyara suturar tare da tubular na roba ko na roba, ba a ba da shawarar yin amfani da abin ɗamara akan fatar ba.

Menene rikitarwa

Bullous epidermolysis na iya haifar da wasu rikice-rikice kamar cututtuka, kamar yadda samuwar kumfa ke sa fata ta zama mai saukin kamuwa da ƙwayoyin cuta da fungi, alal misali. A wasu mawuyacin yanayi, waɗannan ƙwayoyin cuta da suka shiga fatar mutum mai cutar epidermolysis za su iya kaiwa ga jini kuma su bazu cikin sauran jiki, su haifar da sepsis.

Hakanan mutanen da ke fama da cutar epidermolysis bullosa na iya fama da rashin abinci mai gina jiki, wanda ke fitowa daga kumburin baki ko na ƙarancin jini, wanda ke haifar da zubar jini daga raunikan. Wasu matsalolin haƙori, kamar su caries, na iya bayyana, saboda rufin bakin yana da matukar rauni ga mutanen da ke da wannan cutar. Hakanan, wasu nau'ikan epidermolysis bullosa suna kara yawan barazanar kamuwa da cutar kansa ta mutum.