Mawallafi: Morris Wright
Ranar Halitta: 2 Afrilu 2021
Sabuntawa: 22 Yuni 2024
Anonim
Ciwon Wiskott-Aldrich - Kiwon Lafiya
Ciwon Wiskott-Aldrich - Kiwon Lafiya

Wadatacce

Ciwon Wiskott-Aldrich cuta ce ta kwayar halitta, wacce ke daidaita tsarin garkuwar jiki da ke tattare da ƙwayoyin lymphocytes na T da B, da ƙwayoyin jini waɗanda ke taimakawa wajen sarrafa zub da jini, platelets.

Kwayar cututtuka na Wiskott-Aldrich Syndrome

Kwayar cututtukan wiskott-Aldrich na iya zama:

Yanayin zub da jini:

  • Rage lamba da girman platelet a cikin jini;
  • Cututtukan jini na cutane wanda yake da launuka ja-shuɗi masu girman kan fil, wanda ake kira "petechiae", ko kuma suna iya zama manya kuma sun yi kama da rauni;
  • Kujerun jini (musamman a lokacin yarinta), da gumison jini da dogon jini.

Yawan cututtukan da ke haifar da nau'ikan ƙwayoyin cuta kamar:

  • Otitis media, sinusitis, ciwon huhu;
  • Cutar sankarau, ciwon huhu da cutar Pneumocystis jiroveci ta haifar;
  • Kwayar cututtukan fata ta kwayar cutar ta hanyar molluscum contagiosum.

Cancanta:


  • Yawaitar cututtukan fata;
  • Raƙuman duhu akan fata.

Bayanai na Autoimmune:

  • Vasculitis;
  • Anemia na jini;
  • Idiopathic thrombocytopenic tsarkakakke.

Za'a iya yin ganewar asali game da wannan cutar ta likitan yara bayan lura da asibiti na alamun da takamaiman gwaji. Tantance girman platelet na daya daga cikin hanyoyin gano cutar, kasancewar 'yan cutuka kalilan ke da wannan halin.

Jiyya don cututtukan Wiskott-Aldrich

Maganin da yafi dacewa da cututtukan Wiskott-Aldrich shine dashen ɓarna. Sauran nau'ikan magani sune cire saifa, saboda wannan kwayar tana lalata kananan kwayoyin platelets da mutane masu wannan ciwo ke fama da shi, amfani da haemoglobin da kuma amfani da maganin rigakafi.

Tsammani na rayuwa ga mutanen da ke fama da wannan ciwo ba shi da ƙarfi, waɗanda ke rayuwa bayan shekara goma yawanci sukan kamu da ciwace-ciwacen ƙwayoyi irin su lymphoma da leukemia.


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